INTRODUCTION This prospective study was planned to investigate the frequency and relationship of acquired von Willebrand syndrome (AVWS) with aortic and pulmonary stenosis in patients. METHODS A total of 84 children, ranging from two to 18 years of age, were enrolled in this study. Of these, 28 had isolated aortic stenosis, 32 had isolated pulmonary stenosis and 24 were healthy. Children with...

1. Snellen HA, Van Ingen HC, Hoefsmit EChM: Patterns of anomalous pulmonary venous drainage. Circulation 38: 45, 1968 2. Frye RL, Krebs M, Rahimtoola SH, Ongley PA, Hallermann FJ, Wallace RB: Partial anomalous pulmonary venous connection without atrial septal defect. Am J Cardiol 22: 242, 1968 3. Baker CG, Benson PF, Joseph MC, Ross DN: Congenital mitral stenosis. Br Heart J 24: 498, 1962 4. Ni...

Percutaneous pulmonary valvuloplasty was performed in 27 patients with congenital pulmonary valve stenosis. A fall in the transvalve gradient of at least 15 mm Hg occurred in 22 patients. In five there was little change in the severity of the stenosis; in three of these the pulmonary valve was dysplastic. None of the successfully treated patients had a dysplastic valve. The two other failures, ...

Sudden death is now an infrequent occurrence in severe aortic stenosis. However, an impressive increase in pulmonary arteriolar resistance has been found in some patients with end-stage aortic stenosis dying suddenly or deteriorating suddenly after catheterisation. Pulmonary hypertension does not seem to cause sudden death, but, in conjunction with decreased cardiac output, a critical reduction...

abstract hypoplastic right ventricular is a rare congenital heart disease. a few cases have been reported. we presented a case with hypoplastic right ventricular and multiple associated anomaly (ventricular septal defect, atrial septal defect and pulmonary stenosis) in whom the main concern was whether biventricular repair or fontan type surgery would be the optimal management in this patient. ...

with a small ventricular communication, to a large ventricular septal defect dominating the picture with mild obstruction. When the pulmonary stenosis is mild, whether the ventricular septal defect is small or large, a left-to-right shunt is always present, giving the clinical picture of a ventricular septal defect. On the other hand, if the stenosis is severe and the ventricular septal defect ...

Percutaneous pulmonary balloon valvuloplasty is the treatment of choice for pulmonary stenosis but remains difficult to carry out in adults. This is a report on a young adult who was suspected of angina but echocardiogram revealed congenital pulmonary stenosis; safely and effectively treated by balloon valvuloplasty. This report includes a literature review that demonstrates the safety and effi...

A 68-year-old woman with long-standing severe pulmonary arterial hypertension was referred for coronary catheterization for investigation of worsening exertional dyspnea associated with angina. Coronary angiography revealed critical ostial left main coronary artery (LMCA) stenosis. Given the history of severe pulmonary arterial hypertension, simultaneous angiography of the LMCA and main pulmona...

Severe pulmonary stenosis presents early in life; late presentation is rare. Very late presentation like in our case is rarest of rare. Likewise calcification of pulmonary valve is rare. We describe here, one such case in an eighty-one year old female who astonishingly not only tolerated severe form of pulmonary stenosis but had also gone through three full term pregnancy, successfully without ...

Hypertension and episodic pulmonary oedema are known complications of bilateral renovascular disease. However, significant proteinuria has not been reported in this setting. We describe a patient who presented with recurrent pulmonary oedema and nephrotic syndrome, and was found to have bilateral renal artery stenosis. Percutaneous angioplasty and stenting led to a complete resolution of both, ...