نتایج جستجو برای: neuronal degeneration

تعداد نتایج: 172201  

Journal: :Human molecular genetics 2014
Sen Yan Chuan-En Wang Wenjie Wei Marta A Gaertig Liangxue Lai Shihua Li Xiao-Jiang Li

Mutations in TAR DNA-binding protein 43 (TDP-43) are associated with familial forms of amyotrophic lateral sclerosis and frontotemporal lobar degeneration. Although recent studies have revealed that mutant TDP-43 in neuronal and glial cells is toxic, how mutant TDP-43 causes primarily neuronal degeneration in an age-dependent manner remains unclear. Using adeno-associated virus (AAV) that expre...

Journal: :Toxicologic pathology 1997
K Nagashima

As an animal model for examining the pathogenicity of human organic mercury intoxication, rats have been used for the reproduction of human neurologic diseases. Rats experimentally exposed to methylmercury chloride showed clinical signs of neurologic dysfunction characterized by ataxic behavior. Neuropathology of the diseased animals consisted of lesions such as: (a) degeneration of the periphe...

Journal: :Biochemical and biophysical research communications 2008
Gregory D Ford Byron D Ford Ernest C Steele Alicia Gates Darryl Hood Mika A B Matthews Sophia Mirza Peter R MacLeish

The Purkinje cell degeneration (PCD) mutant mouse is characterized by a degeneration of cerebellar Purkinje cells and progressive ataxia. To identify the molecular mechanisms that lead to the death of Purkinje neurons in PCD mice, we used Affymetrix microarray technology to compare cerebellar gene expression profiles in pcd3J mutant mice 14 days of age (prior to Purkinje cell loss) to unaffecte...

2016
Feng Mei Klaus Lehmann-Horn Yun-An A Shen Kelsey A Rankin Karin J Stebbins Daniel S Lorrain Kara Pekarek Sharon A Sagan Lan Xiao Cory Teuscher H-Christian von Büdingen Jürgen Wess J Josh Lawrence Ari J Green Stephen Pj Fancy Scott S Zamvil Jonah R Chan

Demyelination in MS disrupts nerve signals and contributes to axon degeneration. While remyelination promises to restore lost function, it remains unclear whether remyelination will prevent axonal loss. Inflammatory demyelination is accompanied by significant neuronal loss in the experimental autoimmune encephalomyelitis (EAE) mouse model and evidence for remyelination in this model is complica...

Journal: :Pharmacological reports : PR 2013
Kaori Ueda Tsutomu Nakahara Kaori Akanuma Asami Mori Kenji Sakamoto Kunio Ishii

BACKGROUND Neuronal damage leads to capillary degeneration in an N-methyl-D-aspartate (NMDA)-induced retinal degeneration model; however, the mechanisms underlying this phenomenon are not fully understood. The phosphatidylinositol 3-kinase (PI3K)/Akt signaling pathway has been recognized as an intracellular pro-survival signaling system. Therefore, we used the PI3K inhibitors LY294002 and wortm...

Journal: :The Journal of neuroscience : the official journal of the Society for Neuroscience 1989
R Siman J C Noszek C Kegerise

Sustained stimulation of receptors for excitatory amino acids leads to both activation of the calcium-dependent cysteine protease calpain I and to the death of receptive neurons. Here, we have examined the relationship between the calpain I activation and neurodegeneration. Calpain I activation was manifested as increased levels of the major proteolytic fragments of the calpain substrate spectr...

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