Adenoid cystic carcinoma is a malignant neoplasm arising from the salivary glands. The most striking feature of this tumor is that it is locally aggressive, with perineural invasion, tendency to metastasize, high recurrence rates. The parotid gland is the most commonly affected site in the head and neck region, tongue being relatively rare. The current study presents a rare case of 6 years old ...

Malignant fibrous histiocytoma (MFH) usually presents in the extremities or retroperitoneum. Cases involving the kidney are rare and portend a poor prognosis. Although radical nephrectomy is the most beneficial curative choice for this neoplasm, patients are often treated with adjuvant chemotherapy due to high risk of local recurrence and distant metastases. We describe a case of a 68-year-old ...

Two cases of Lhermitte-Duclos disease (LDD), one associated with Cowden's disease, are reported. Both demonstrated recurrence long after initial surgical resection. There is a propensity for occurrence in the left cerebellar hemisphere. On MR there is hypointensity on T1-weighted images and moderately high signal on T2-weighted images, with parallel linear striations on the surface of the lesio...

Rhabdoid meningioma is a rare aggressive variant of meningioma, regarded as WHO grade III type. Histologically and cytologically, it is distinctive type having abundant eosinophilic cytoplasm, cytoplasmic inclusion with eccentrically placed vesicular nuclei and prominent nucleoli. High recurrence rate and poor outcome are important features. Here we are presenting a rare case of rhabdoid mening...

Pilomatrix Carcinoma (PC) is an exceedingly rare neoplasm. Although it has been described at various anatomical sites, fewer than 25 cases have been reported in the face and scalp. Although early recognition and treatment is paramount in optimization of outcomes for this aggressive carcinoma, the diagnosis is complicated by shared features with its more common benign counterpart. In patients wi...

Vulvar aggressive angiomyxoma (AA) is a rare mesenchymal tumor of the vulva. Due to its slow-growing nature, it is often overlooked and misdiagnosed by primary care providers (PCPs). We describe a case report of vulvar AA in a 38-year-old woman who underwent complete surgical excision of the neoplasm with no evidence of recurrence on a 5-year followup. A literature review follows to provide PCP...

Context Intraductal Papillary Mucinous Neoplasm of the pancreas is an increasingly diagnosed neoplasm that rarely penetrates adjacent organs. Case report A sixty-year-old asymptomatic male was seen for evaluation of iron deficiency anemia. Patient was found to have a mucin secreting tumor during esophagogastroduodenoscopy. Computed tomography scan showed an enlarged pancreas with numerous focal...

Ameloblastoma is a true neoplasm of odontogenic origin and benign in nature. But it has a high percentage of local recurrence with possible malignant development when treated inadequately. The treatment planning in ameloblastomas is still not clear. We describe a case report of unicystic plexiform ameloblastoma in a young girl who was treated with conservative surgical management (enucleation &...

Basosquamous carcinoma is a rare tumor with features of both basal cell and squamous cell carcinoma, linked by a transition area. It is a rare epithelial neoplasm with a tendency for local recurrence. It also has a high incidence of distant metastasis, a condition that differentiates it from the basal cell carcinoma. In this case, the slow course of the infiltrative lesion associated to patient...

The calcifying epithelial odontogenic tumor (CEOT) is a rare benign neoplasm; it comprises only 0.6 % to 1.7 % of all odontogenic tumors. Most cases involve the posterior mandible; there have been few reported maxillary cases. Although its biological behavior is relatively indolent, maxillary lesions tend to grown rapidly and not be circumscribed. Treatment of the CEOT consists of surgical remo...