نتایج جستجو برای: misfolded structure

تعداد نتایج: 1570813  

Journal: :Molecular biology of the cell 2009
Meredith Boyle Metzger Susan Michaelis

ER quality control (ERQC) prevents the exit of misfolded secretory and membrane proteins from the ER. A critical aspect of ERQC is a transcriptional response called the unfolded protein response (UPR), which up-regulates genes that enable cells to cope with misfolded, ER-retained proteins. In this study, we compare the transcriptional responses in yeast resulting from the acute expression of mi...

2017
Paola Rusmini Riccardo Cristofani Mariarita Galbiati Maria E. Cicardi Marco Meroni Veronica Ferrari Giulia Vezzoli Barbara Tedesco Elio Messi Margherita Piccolella Serena Carra Valeria Crippa Angelo Poletti

Amyotrophic lateral sclerosis (ALS) and spinal and bulbar muscular atrophy (SBMA) are two motoneuron diseases (MNDs) characterized by aberrant protein behavior in affected cells. In familial ALS (fALS) and in SBMA specific gene mutations lead to the production of neurotoxic proteins or peptides prone to misfold, which then accumulate in form of aggregates. Notably, some of these proteins accumu...

Journal: :The EMBO journal 2009
Antje Schäfer Dieter H Wolf

Endoplasmic reticulum-associated degradation (ERAD) is a cellular pathway for the disposal of misfolded secretory proteins. This process comprises recognition of the misfolded proteins followed by their retro-translocation across the ER membrane into the cytosol in which polyubiquitination and proteasomal degradation occur. A variety of data imply that the protein import channel Sec61p has a fu...

2012
Tomohiko Aoe

The endoplasmic reticulum (ER) provides a folding environment for newly synthesized secretory and membrane proteins (Ellgaard and Helenius, 2003). Secretory proteins are synthesized by ribosomes and translocated cotranslationally or posttranslationally to the ER. These newly synthesized proteins interact with ER molecular chaperones, such as immunoglobulin heavy chain-binding protein (BiP), cal...

Journal: :Cell 2005
Ian J. MacRae Jennifer A. Doudna

The Ro 60 kDa autoantigen binds misfolded RNAs and likely functions in small RNA quality control. In this issue of Cell, Stein et al. (2005) present crystal structures of Ro alone and bound to both double- and single-stranded RNA, revealing two distinct RNA binding sites that suggest how Ro may distinguish between native and misfolded small RNAs.

Journal: :Journal of the American Chemical Society 2008
Jaime Curtis-Fisk Ryan M Spencer David P Weliky

Inclusion bodies are insoluble aggregates that are formed by bacteria to store excess recombinant protein produced during expression. The structure of the protein in inclusion bodies is poorly understood but it has been hypothesized that the protein may form misfolded beta sheet aggregates. This paper presents an isotopic labeling and solid-state nuclear magnetic resonance approach to determine...

پایان نامه :دانشگاه تربیت معلم - تهران - دانشکده علوم 1393

in this thesis, structural, electronical, and optical properties of inverse pervskite(ca3pbo) in cubic phase have been investigated.the calculation have been done based on density functional theory and according to generalized gradiant approximate (gga) as correlating potential. in order to calculate the configurations, implementing in the wien2k code have been used from 2013 version. first of ...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید