نتایج جستجو برای: ldlr locus

تعداد نتایج: 69565  

Journal: :Biochimica et biophysica acta 2013
J C Souza E C Vanzela R A Ribeiro L F Rezende C A de Oliveira E M Carneiro H C F Oliveira A C Boschero

AIMS/HYPOTHESIS Changes in cellular cholesterol level may contribute to beta cell dysfunction. Islets from low density lipoprotein receptor knockout (LDLR(-/-)) mice have higher cholesterol content and secrete less insulin than wild-type (WT) mice. Here, we investigated the association between cholesterol content, insulin secretion and Ca(2+) handling in these islets. METHODS Isolated islets ...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2002
Donald L Gillian-Daniel Paul W Bates Angie Tebon Alan D Attie

Mutations in the low density lipoprotein (LDL) receptor (LDLR) cause hypercholesterolemia because of inefficient LDL clearance from the circulation. In addition, there is a paradoxical oversecretion of the metabolic precursor of LDL, very low density lipoprotein (VLDL). We recently demonstrated that the LDLR mediates pre-secretory degradation of the major VLDL protein, apolipoprotein B (apoB). ...

Journal: :Nature communications 2016
Paulina Bartuzi Daniel D Billadeau Robert Favier Shunxing Rong Daphne Dekker Alina Fedoseienko Hille Fieten Melinde Wijers Johannes H Levels Nicolette Huijkman Niels Kloosterhuis Henk van der Molen Gemma Brufau Albert K Groen Alison M Elliott Jan Albert Kuivenhoven Barbara Plecko Gernot Grangl Julie McGaughran Jay D Horton Ezra Burstein Marten H Hofker Bart van de Sluis

The low-density lipoprotein receptor (LDLR) plays a pivotal role in clearing atherogenic circulating low-density lipoprotein (LDL) cholesterol. Here we show that the COMMD/CCDC22/CCDC93 (CCC) and the Wiskott-Aldrich syndrome protein and SCAR homologue (WASH) complexes are both crucial for endosomal sorting of LDLR and for its function. We find that patients with X-linked intellectual disability...

ژورنال: Medical Laboratory Journal 2012
Alizadeh Sharg Sh, , Dolatkhah H, , Movahedian A, , Rahmani S Z, ,

Abstract Background and objectives: Familial hypercholesterolemia (FH) is an autosomal disorder characterized by increased levels of total cholesterol and low density lipoprotein cholesterol. The FH clinical phenotype has been associated with increased risk of coronary heart disease and premature death. The mutation in LDLR gene in most cases is responsible for FH phenotype. Furthermore, other ...

Journal: :Circulation research 2015
Kevin M Patel Alanna Strong Junichiro Tohyama Xueting Jin Carlos R Morales Jeffery Billheimer John Millar Howard Kruth Daniel J Rader

RATIONALE Noncoding gene variants at the SORT1 locus are strongly associated with low-density lipoprotein cholesterol (LDL-C) levels, as well as with coronary artery disease. SORT1 encodes a protein called sortilin, and hepatic sortilin modulates LDL metabolism by targeting apolipoprotein B-containing lipoproteins to the lysosome. Sortilin is also expressed in macrophages, but its role in macro...

2011
Serena Sanna Bingshan Li Antonella Mulas Carlo Sidore Hyun M. Kang Anne U. Jackson Maria Grazia Piras Gianluca Usala Giuseppe Maninchedda Alessandro Sassu Fabrizio Serra Maria Antonietta Palmas William H. Wood Inger Njølstad Markku Laakso Kristian Hveem Jaakko Tuomilehto Timo A. Lakka Rainer Rauramaa Michael Boehnke Francesco Cucca Manuela Uda David Schlessinger Ramaiah Nagaraja Gonçalo R. Abecasis

Complex trait genome-wide association studies (GWAS) provide an efficient strategy for evaluating large numbers of common variants in large numbers of individuals and for identifying trait-associated variants. Nevertheless, GWAS often leave much of the trait heritability unexplained. We hypothesized that some of this unexplained heritability might be due to common and rare variants that reside ...

Journal: :Atherosclerosis 2016
Justine A Maedeker Kellie V Stoka Siddharth A Bhayani William S Gardner Lisa Bennett Jesse D Procknow Marius C Staiculescu Tezin A Walji Clarissa S Craft Jessica E Wagenseil

BACKGROUND AND AIMS High blood pressure and reduced aortic compliance are associated with increased atherosclerotic plaque accumulation in humans. Animal studies support these associations, but additional factors, such as fragmented elastic fibers, are present in most previous animal studies. Elastin heterozygous (Eln+/-) mice have high blood pressure and reduced aortic compliance, with no evid...

Journal: :Journal of lipid research 2004
Sung-Joon Lee Itamar Grosskopf Sungshin Y Choi Allen D Cooper

Apolipoprotein E2 (apoE2) and apoE3-Leiden cause chylomicron remnant accumulation (type III hyperlipidemia). However, the degree of dyslipidemia and its penetrance are different in humans and mice. Remnant uptake by isolated liver from apoE-/- mice transgenic for human apoE2, apoE3-Leiden, or apoE3 was measured. In the presence of both LDL receptor (LDLR) and LDL receptor-related protein (LRP),...

2015
Paulette A Krishack Clarissa V Bhanvadia John Lukens Timothy J Sontag Maria C De Beer Godfrey S Getz Catherine A Reardon

BACKGROUND Atherosclerosis is a chronic inflammatory disorder, and several studies have demonstrated a positive association between plasma serum amyloid A (SAA) levels and cardiovascular disease risk. The aim of the study was to examine whether SAA has a role in atherogenesis, the underlying basis of most cardiovascular disease. METHODS AND RESULTS Mice globally deficient in acute-phase isofo...

Journal: :Cardiovascular research 2016
Karthikeyan Krishnamurthy Shannon Glaser Gianfranco D Alpini Arturo J Cardounel Zhenguo Liu Govindasamy Ilangovan

AIMS Stress response, in terms of activation of stress factors, is known to cause obesity and coronary heart disease such as atherosclerosis in human. However, the underlying mechanism(s) of these pathways are not known. Here, we investigated the effect of heat shock factor-1 (HSF-1) on atherosclerosis. METHODS AND RESULTS HSF-1 and low-density lipoprotein receptor (LDLr) double knockout (HSF...

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