Case description: In case 1, a 17-year-old woman presented hard and painless swelling in the left posterior mandible. Radiographically, a radiolucent area with a radiopaque was observed. A clinical diagnosis of ameloblastoma or odontogenic keratocystic tumor was established. The histopathological examination revealed an orthokeratinized odontogenic cyst. In case 2, a 23-year-old woman presented...

The Nevoid Basal Cell Carcinoma Syndrome (NBCCS) is an uncommon disorder caused by a mutation in Patched, tumor suppressor gene. It is mainly characterized by numerous early onset basal cell carcinomas, odontogenic cysts of jaw and skeletal abnormalities. Due to the wide clinical spectrum, treatment and management of its modalities are not standardized and should be individualized and monitored...

Em 2005, a Organização Mundial de Saúde revisou e atualizou a classificação dos tumores odontogênicos, e algumas terminologias foram modificadas. Devido à sua natureza neoplásica, o ceratocisto odontogênico, anteriormente classificado como um cisto, teve seu nome alterado para tumor odontogênico ceratocístico (TOC). A prevalência de TOC no seio maxilar é de apenas 1%.1 O TOC possui taxa elevada...

The Odontogenic Keratocyst (OKC), first described by Phillipsen in 1956, has been reclassified as odontogenic neoplasm and has been renamed as Keratocystic Odontogenic Tumor (KCOT) as reported in WHO classification of head and neck tumors in 2005. Odontogenic keratocysts are benign intraosseous tumors of odontogenic origin that occur most commonly in the jaw. In particular, they have a predilec...

Keratocystic odontogenic tumors (KCOTs), formally known as odontogenic keratocysts, are benign developmental tumors that are found primarily in the mandibular molar region and ascending ramus. The disease is characterized by aggressive growth and a high recurrence rate following surgical treatment. The present study reports the rare case of a 25-year-old male with a giant KCOT involving the rig...