The superior mesenteric artery syndrome (SMAS) is an uncommon condition in children. We describe a case of a 7-year-old boy with SMAS that occurred 3 years after a Deloyers' procedure for subtotal colonic Hirschsprung who was admitted for bilious vomit, abdominal pain and diarrhea due to unrecognized celiac disease. This case emphasize that SMAS in children needs a close medical and surgical fo...

In 1886, Harald Hirschsprung first described two cases of infantile constipation with colonic dilation, but he did not suggest any etiology or therapeutic option. Over the past 30 years, many studies have revealed the clinical presentation, radiological and histological diagnoses, surgical procedures, epidemiology, and associated genetics related to colonic dilation. Hirschsprung’s disease (HD)...

La enfermedad de Hirschsprung fue descrita por el pediatra danés Harald en 1888, edses la neuropatía entérica congénita más común, donde se produce una ausencia relajación del musculo entérico, con posterior obstrucción intestinal, esta caracterizada células ganglionares los plexos mientérico y submucoso intestino grueso, Su etiopatogenia está dada aganglionosis tracto digestivo, afectando prin...

THE DEVELOPMENT of a successful surgical treatment for Hirschsprung's disease 11 and the establishment of a sound pathologic and etiologic basis 3 for the disease have been among the most gratifying events in Pediatric Surgery of the last decade. The result has been to render accurate diagnosis possible with precision. At the same time the knowledge that an effective surgical treatment is avail...