PURPOSE To compare the Percentage of Consonants Correct (PCC) index of children with and without hearing loss, and to verify whether the time using hearing aids, the time in therapy, and the time spent until hearing loss was diagnosed influence the performance of deaf children. METHODS Participants were 30 children, 15 with hearing impairment and 15 with normal hearing, paired by gender and a...

Purpose: To compare the Percentage of Consonants Correct (PCC) index of children with and without hearing loss, and to verify whether the time using hearing aids, the time in therapy, and the time spent until hearing loss was diagnosed influence the performance of deaf children. Methods: Participants were 30 children, 15 with hearing impairment and 15 with normal hearing, paired by gender and a...

Osteogenesis imperfecta (OI) is an inherited bone and connective tissue disorder associated with the lifelong occurrence of frequent fractures following even mild trauma. Hearing loss is frequently reported in patients with OI. Objective: to examine the ratio of hearing loss in children with OI, and the relationship between audiological findings and CT images of temporal bone in children with O...

The Canadian Hearing and Auditory Research Translation (CHART) group is a newly formed taskforce to develop collaborative research initiatives. Initial discussions centered on diagnostic improvements for middle ear disease, auditory neuropathy spectrum disorder, tinnitus and presbycusis. Central to these discussions was the widely held view that the standard audiogram and its interpretation is ...

Fabry disease is an X-linked inherited disorder of glycosphingolipid metabolism due to the deficient activity of a lysosomal enzyme, alpha-galactosidase A. The resultant systemic accumulation of sphingolipids can lead to progressive and sudden hearing loss alongside renal, cardiac and cerebrovascular complications. Although replacement therapy seems to be beneficial for cochlear function, few d...

Mucopolysaccharidosis (MPS) is a genetic, progressive and clinically heterogeneous disorder that usually involves multiple body systems due to the deficiency of one enzymes play role in metabolism glycosaminoglycans (GAGs), which accumulates lysosomes organs. It wide spectrum clinical manifestations. Hearing dysfunction well known association found most patients with can’t be underestimated as ...

RESULTS Out-patient and in-patient caseloads differ between the two services: 27% of the deaf out-patient caseload have schizophrenia, schizotypal and delusional disorders (compared with 19% of hearing patients) and 19% have neurotic, stress-related and somatoform disorders (compared with 8% of hearing patients). The general psychiatric service out-patient case-load had rates of 8% and 43% for ...

Sarcoidosis is an inflammatory multisystem disorder of unknown cause. Approximately 5-7% of patients manifest symptoms of central nervous system involvement, or neurosarcoidosis. Cranial neuropathy usually entails facial nerve palsy and optic neuritis. Sudden hearing loss has been reported in fewer than 20 cases. Herewith, two new cases of sudden hearing loss due to probable neurosarcoidosis ar...