Abstract Pulmonary agenesis is a rare malformation associated with congenital heart disease and may lead to life-threatening condition death without pre-planned surgical medical support. We report an unusual case of unilateral pulmonary in combination total anomalous venous connection, complete vascular ring, retroaortic, retroesophageal innominate vein, secondary atrial septal defect, which wa...

Background Congenital Heart Disease and Rheumatic Heart Disease are the most common childhood cardiac disease encountered in developing countries. Objective To study the pattern and the prevalence of cardiac diseases, its age wise distribution and to determine their risk factors for mortality in children presented to Dhulikhel Hospital, Kathmandu University Hospital. Method A study of cardiac d...

Congenital heart malformations are the most common type of defects found at birth. About 1% of infants are born with one or more heart defect on a yearly basis. Congenital Heart Disease (CHD) causes more deaths in the first year of life than any other congenital abnormality, and each year, nearly twice as many children die in the United States from CHD as from all forms of childhood cancers com...

Method 2013-2014: 23 congenital cardiac patients underwent heart transplantation. 13 of them: previous univentricular palliation: hypoplastic left heart syndrome (n = 8), dtransposition of great arteries+criss-cross-heart (n = 1), unbalanced atrioventricular septal defect (n = 1), pulmonary atresia+intact ventricular septum (n = 1) and grown-up patients (GUCH) (n = 2: 1 double-inlet-leftventric...

Shinebourne, E. A., Haworth, S. G., Anderson, R. H., and Ulgur, A. (1974). Archives of Disease in Childhood, 49, 729. Differential diagnosis of congenital heart disease in the first 3 months of life: significance of a superior (left) QRS axis. The ECGs of 473 infants under the age of 3 months who were referred to a paediatric cardiological unit were analysed; 47 (10%) of the ECGs showed a super...

Electron beam angiography (EBA) provides excellent anatomic imaging in patients with congenital heart disease and may be useful in the assessment of atrial septal defects (ASDs). We present four patients with an ASD who were considered for percutaneous closure and underwent EBA for measurement of defect size and assessment of rim adequacy, adjacent cardiac structures, and associated congenital ...

C S i o the Editor: An estimated 80% of congenital heart defects result rom an interaction between susceptibilities in parental and fetal enomes and environmental exposures including maternal lifestyle actors (1). We and others have recently reported that women who ave congenital heart defect-affected pregnancies have alterations n folate metabolism (2). This population-based case-control study...

Published reports and personal experience are reviewed relating to patients under 1 year of age diagnosed with a vein of Galen malformation and congenital heart disease. Including five patients from this institution, a total of 23 patients (12 neonates) with congenital heart disease and a vein of Galen malformation have been reported. Six of these had sinus venosus atrial septal defect and nine...

Motivated by the inadequacy of nonsurgical therapy in ameliorating congenital cardiac disease, surgical pioneers in the 1940s and 1950s began to develop techniques that would allow for the intracardiac repair of congenital heart disease. The fi rst operation on the open human heart under direct vision—closure of an atrial septal defect (ASD) in a 5-year-old girl—was performed at the University ...