Arrhythmogenic right ventricular dysplasia (ARVD) is an inheritable heart muscle disease that predominantly affects the right ventricle (RV) and predisposes to ventricular arrhythmias and sudden cardiac death (SCD)1. The natural history is predominantly related to ventricular electric instability which may lead to arrhythmic SCD, mostly in young people and athletes2,3, but may progress with sig...

From the Card of Medicine, Miam rado Health Scien Program, Univers do; Howard Hug ter of Brigham & Massachusetts an Medicine, Houston Manuscript rec January 22, 2009; Reprint request School of Medicin 33101-5138. E-ma No conflicts of 1071-9164/$ s 2009 Elsevie doi:10.1016/j.ca Substantial progress has been made recently in understanding the genetic basis of cardiomyopathy. Cardiomyopathies with...

Atherosclerotic renovascular disease (ARVD) is increasingly recognised as an important cause of both chronic and end stage renal failure. These patients tend to do badly on dialysis, which reflects their systemic atherosclerotic burden. In an eVort to delay and perhaps prevent their need for renal replacement therapy, some patients are subjected to a variety of medical, radiological and surgica...

The presence of pacemakers and implantable cardioverter-defibrillators (ICD) is considered historically a contraindication to magnetic resonance (MR) imaging. This image modality has unparalleled soft-tissue imaging capabilities, and many consider it as the image of choice for patients with arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C). ICDs are now smaller, with less magne...

Arrhythmogenic right ventricular dysplasia ARVD is a disorder which is characterized by replacement of right ventricular myocardium by fat and fibrous tissue. Although it generally causes arrhythmias originating from the right ventricle, sudden deaths might be seen. A 30-year-old woman with no previous symptoms of a particular disorder was found dead in her house. The organs of her body were se...

BACKGROUND Randomized controlled trials (RCT) have shown no overall benefit of renal revascularization in atherosclerotic renovascular disease (ARVD). However, 25% of patients demonstrate improvement in renal function. We used the ratio of magnetic resonance parenchymal volume (PV) to isotopic single kidney glomerular filtration rate (isoSKGFR) ratio as our method to prospectively identify "imp...