نتایج جستجو برای: ترکیبات pah

تعداد نتایج: 30069  

چکیده زمینه  و هدف: هیدروکربن های آروماتیک چند حلقه ای[1] از مهم ترین  آلاینده های محیط می باشند که نشت آن ها از خاک به منابع آب زیرزمینی یکی از مهم ترین  نگرانیهای محیط زیستی می باشد. با توجه به حجم بالای فعالیت های نفتی، سایت های متعددی در کشور آلوده به ترکیبات نفتی شده اند. تصمیم گیری در خصوص پالایش یا عدم پالایش خاک های آلوده به مواد نفتی با توجه به هزینه های بسیار بالای پالایش خاک نیازمند ...

Background: Phenylketonuria (PKU), the most common inborn error of aminoacid metabolism, is an autosomal recessive disorder caused by more than 600 mutations in Phenylalanine Hydroxylase gene (PAH). Distribution pattern of mutations in the PAH gene are specific to each population. The aim of this study was to identify mutations in exons 10 and 11 of the PAH gene in patients with PKU from Golest...

Journal: :evidence based care 0
milad azami md, medical student, student research committee, ilam university of medical sciences, ilam, iran askar sufi nia md, cardiologist, department of cardiology, faculty of medicine, ilam university of medical sciences, ilam, iran mohammad hossein yektakooshali b.sc. in radiology technology, student research committee, school of nursing, midwifery and paramedicine, guilan university of medical sciences, rasht, iran sasan nikpay b.sc, laboratory student, student research committee, ilam university of medical sciences, ilam, iran yaeghoob madmoli student of nursing, student research committee of dezful university of medical sciences, dezful, iran mohammad malekshahi md, medical student, student research committee, ilam university of medical sciences, ilam, iran

pulmonary arterial hypertension (pah) is a progressive disease with high morbidity and mortality rates. research has shown that pah has a prevalence rate of 10-79% in thalassemia major patients. this cross-sectional study was carried out in 2014 to determine the prevalence and risk factors of pah in all thalassemia major patients of over 18 years of age in ilam, iran. a cardiologist measured sy...

Journal: :Molecular genetics and metabolism 2001
M Lindner D Haas E Mayatepek J Zschocke P Burgard

Recently, BH(4)-responsive phenylalanine hydroxylase (PAH) deficiency was reported in patients with specific mutations in the PAH gene, and it was suggested that BH(4) responsiveness may be determined by the respective genotypes. We now report on three patients with PAH deficiency and the same genotype but different responses to standardized BH(4) loading. Our results suggest that BH(4) respons...

2017
Konstantinos Dimopoulos Lisa Parfitt

Congenital heart disease (CHD) is one of the most common causes of pulmonary arterial hypertension (PAH), with a prevalence nearing that of idiopathic PAH in registries. Despite similarities in pulmonary vascular pathology, PAHCHD differs from idiopathic PAH and other types of PAH. In fact, PAH-CHD is a term that includes a wide spectrum of conditions and pathophysiologies, ranging from Eisenme...

2005
Jason X. - J. Yuan Lewis J. Rubin

Pulmonary hypertension can be classified into 4 categories: pulmonary arterial hypertension (PAH), pulmonary venous hypertension, pulmonary hypertension associated with hypoxemia, and pulmonary hypertension due to chronic thrombotic or embolic disease. PAH is a progressive and often fatal condition that predominantly affects women. Approximately 10% of patients diagnosed with PAH without a demo...

Journal: :Circulation journal : official journal of the Japanese Circulation Society 2013
Yoshihiro Fukumoto Norikazu Yamada Hiromi Matsubara Minori Mizoguchi Kazuaki Uchino Atsushi Yao Yasuki Kihara Mitsuhiro Kawano Hiroshi Watanabe Yutaka Takeda Takeshi Adachi Shinobu Osanai Nobuhiro Tanabe Teruo Inoue Akihiro Kubo Yuri Ota Koichiro Fukuda Takeshi Nakano Hiroaki Shimokawa

BACKGROUND We have previously demonstrated that long-term inhibition of Rho-kinase ameliorates pulmonary arterial hypertension (PAH) in animal models. In the present study, we examined the clinical effects of mid-term oral treatment with an extended release formulation of AT-877 (fasudil hydrochloride), a specific Rho-kinase inhibitor (AT-877ER) on PAH. METHODS AND RESULTS 23 PAH patients wer...

Journal: :American journal of physiology. Lung cellular and molecular physiology 2014
Tim Lahm Rubin M Tuder Irina Petrache

Pulmonary arterial hypertension (PAH) is a devastating and progressive disease with marked morbidity and mortality. Even though being female represents one of the most powerful risk factors for PAH, multiple questions about the underlying mechanisms remain, and two "estrogen paradoxes" in PAH exist. First, it is puzzling why estrogens have been found to be protective in various animal models of...

2013
Sébastien Renard Roxane Paulin Sandra Breuils-Bonnet Serge Simard Philippe Pibarot Sébastien Bonnet Steeve Provencher

Provirus integration site for Moloney murine leukemia virus (Pim-1) is an oncoprotein overexpressed in lungs from pulmonary arterial hypertension (PAH) patients and involved in cell proliferation via the activation of the NFAT/STAT3 signaling pathway. We hypothesized that Pim-1 plasma levels would predict the presence of PAH and correlate with disease severity. Pim-1 plasma levels were measured...

2011
Paulina Mocchiutti María V. Galván María C. Inalbon Miguel A. Zanuttini

Polyelectrolytes containing amine functional groups such as PAH (poly(allylamine hydrochloride)) can be useful, under certain conditions, for improving paper strength. In this work, the charge density of PAH was determined at different pH and ionic strengths; PAH adsorption onto the cellulosic fibers was characterized, and the effects of low PAH dosage on the papermaking properties were evaluat...

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