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Granulomatosis with polyangiitis (GPA; previously Wegener granulomatosis) is a rare, multisystem, necrotizing granulomatous vasculitis that classically affects the upper and lower respiratory tracts and kidneys but can have diverse clinical features. The clinical course is often rapidly progressive, and without appropriate treatment is almost universally fatal. Early symptoms are often nonspeci...

The association of juvenile idiopathic arthritis (JIA) and Wegener granulomatosis (WG) is extremely rare. To date, only 3 patients with JIA accompanied by WG were described in the literature. Here we report a girl who had been followed-up for RF positive JIA for 3 years and developed WG at the age of 15. She started suffering from symmetrical arthritis of knees and wrists when she was 12. The t...