A 13-year-old girl with Turner's syndrome and bleeding from intestinal venous ectasia is reported. The various types of vascular anomaly of the bowel associated with Turner's syndrome are discussed. Awareness of these anomalies may help prevent unnecessary laparotomy in children with this syndrome.

Partial anomalous pulmonary venous connection (PAPVC) causes a left-to-right shunt from the anomalous pulmonary vein (PV) to a systemic vein. We report an uncommon adult case of PAPVC, in which the left upper PV drained into both the innominate vein and the left atrium (LA), demonstrating retrograde shunting from the LA to the innominate vein. The anomaly was surgically repaired.

We acknowledge the letter from Murakami and colleagues about our article, “Bilateral Superior Venae Cavae With Crisscross Atrial Drainage.” In that article, we documented a rare thoracic systemic venous drainage anomaly in which a persistent left superior vena cava was seen draining into the right atrium (RA) via the coronary sinus and the right superior vena cava (RSVC) draining into the left ...

Arteriovenous malformations (AVMs) are the most common spinal vascular anomaly. The majority are intradural and are supplied by the spinal arteries. This paper presents an unusual A VM that was fed by the lumbar arteries and was located totally in the extradural space; in fact, its drainage enlarged the internal vertebral venous plexus, resulting in its clinical presentation as a right lumbar r...

Persistent left superior vena cava represents a congenital venous anomaly that poses a particular obstacle to the implantation of cardiac rhythm management devices. In the present report we briefly describe the rightsided implantation of a biventricular defibrillator in a patient with persistent left superior vena cava. We also briefly discuss the technically challenging procedures applied in s...

Precordial echocardiography showed two membranes obstructing pulmonary venous return in the left atrium of a 9 month old infant. This anomaly has not previously been described; therefore transoesophageal echocardiography was performed at the time of surgery. This confirmed the anatomy and aided complete resection of both membranes. Even in small infants transoesophageal echocardiography can pro...

A 53-year-old patient with corrected transposition of the great arteries developed complete heart block with fainting episodes. After temporary pacing through the endocardium of the venous (anatomically left) ventricle, a permanent epicardial pacemaker was implanted. This case shows the progressive nature of the atrioventricular conduction disturbances, which are very common in association with...

Received August 8, 2002 Abstract Pulmonary sequestration is a congenital anomaly of lung parenchyma without a normal connection to the tracheobronchial tree and an anomalous systemic arterial supply. We report an 11-month-old boy with extralobar pulmonary sequestration. Magnetic resonance angiogram identified the arterial supply from aorta and venous drainage to azygous vein. Various imaging te...

Blue rubber bleb nevus syndrome (BRBNS) is a rare vascular anomaly syndrome consisting of multifocal venous malformations (VM). The malformations are most. prominent in the skin, soft tissues and gastrointestinal (GI) tract. Chronic bleeding induced by the vascular malformation (VM) lesions in gastrointestinal (GI) tract was the main clinical problem which should be treated. In this paper, two ...

Persistent left superior vena cava (LSVC) is the commonest congenital anomaly of the thoracic venous system. It is within the group of anomalous systemic venous return (ASVR) and the group is subdivided in cephalic, involving the superior vena cava (SVC) and caudal, involving the inferior vena cava (IVC) types. It is also important to recognise that there can be a persistent LSVC with or withou...