congenital muscular dystrophy (cmd)  is an umbrella term collecting a heterogeneous groups of genetic disorders , mostly with autosomal recessive mode of inheritance , and are characterized by muscle weakness since birth or in early infancy , with a dystrophic pattern on muscle biopsy . these children are usually hypotonic and may have joint contractures . the serum creatine kinase level can be...

Autoerythrocyte sensitization syndrome CABS) is a rare purpuric disorder of women characterized by inflammatory and painful ecchymotic lesions unrelated to blood clotting or vascular abnormalities. Gastrointestinal bleeding, hematuria, headache or syncopal attacks may also be observed. Our patient is a 33-year-old woman presenting with recurrent severe painful ecchymotic lesions on both lo...

In order to incorporate the effect of gravity waves (GWs) on the atmospheric circulation most global circulation models (GCMs) employ gravity wave parameterization schemes. To date, GW parameterization schemes in GCMs are used without experimental validation of the set of global parameters assumed for the GW launch spectrum. This paper focuses on the Warner and McIntyre GW parameterization sche...

C onservationists must make hard choices about where to invest limited resources for the protection of biological diversity. Numerous prioritization schemes have identified places where biodiversity is especially rich or risks are especially urgent (1). Application of return on investment (ROI) thinking promises to make conservation investments much more efficient by explicitly incorporating ec...

Current snowmelt parameterisation schemes are largely untested in warmer maritime snowfields, where physical snow properties can differ substantially from the more common colder snow environments. Physical properties such as snow density influence the thermal properties of snow layers and are likely to be important for snowmelt rates. Existing methods for incorporating physical snow properties ...

P2P networks suffer from the free-riding problem, wherein users connect to the network only to use the resources, but do not donate any resources themselves. A popular approach to overcome this problem is to reward peers who share their resources, through payments. This has given a fresh lease of life to micropayments schemes, which are now being used in such networks. P2P Micropayment schemes ...