نتایج جستجو برای: musculoskeletal als

تعداد نتایج: 56606  

2002
Florian Matthes Vanda Lehel

Wir betrachten persönliches Wissen, private Informationen und persönliche Zertifikate als wesentliche Assets, die eine Person in ihren Rollen als Mitarbeiter, als Bürger, als Familienmitglied, als Lernender, als Vereinsmitglied etc. sammelt und mit anderen Mitgliedern dieser persönlichen sozialen Netzwerke rollenbasiert und aufgabenorientiert teilen möchte. Ausgehend von dieser individuellen un...

Journal: :Neuroscience letters 2015
Merryn Brettle Alexandra K Suchowerska Sook W Chua Lars M Ittner Thomas Fath

Amyotrophic lateral sclerosis (ALS) is the most common motor neuron disease and familial ALS accounts for 10% of cases. The identification of familial ALS mutations in the actin-binding protein profilin 1 directly implicates actin dynamics and regulation in the pathogenesis of ALS. The mechanism by which these mutations cause ALS is unknown. In this study we show that expression of the ALS-asso...

2017
Y-H Taguchi Hsiuying Wang

Amyotrophic lateral sclerosis (ALS) is a fatal neurodegenerative disease. An ALS drug, Riluzole, has been shown to induce two different anticancer effects on hepatocellular carcinoma (HCC). In light of this finding, we explore the relationship between ALS and cancer, especially for HCC, from the molecular biological viewpoint. We establish biomarkers that can discriminate between ALS patients a...

2013
Jin Hee Shin Jae Keun Lee

Amyotrophic lateral sclerosis (ALS) is an adult-onset neurological disorder with higher selectivity in the degeneration of the upper and lower motor neurons, which leads to progres‐ sive paralysis of voluntary muscles. Although most cases fall under sporadic ALS (sALS), 10% of cases are inherited and known as familial ALS (fALS). The etiology of most ALS cases remains unknown, but mutations of ...

Journal: :Journal of neuromuscular diseases 2014
Satoshi Yamashita Akiko Fujimoto Yukiko Mori Tomoo Hirahara Akira Mori Teruyuki Hirano Yasushi Maeda Makoto Uchino Yukio Ando

The mechanisms by which amyotrophic lateral sclerosis (ALS) causes motor neuron degeneration remain unknown. We present the case of a 77-year-old Japanese female with clinically probable ALS, who developed ALS symptoms 41 years after onset of myasthenia gravis (MG). We concluded that neither the relapse of MG nor the adverse effects of anti-cholinesterase medication aggravated her symptoms. Alt...

2017
Elisa Longinetti Daniela Mariosa Henrik Larsson Weimin Ye Caroline Ingre Catarina Almqvist Paul Lichtenstein Fredrik Piehl Fang Fang

OBJECTIVE To estimate risks of neurodegenerative and psychiatric diseases among patients with amyotrophic lateral sclerosis (ALS) and their families. METHODS We conducted a register-based nested case-control study during 1990-2013 in Sweden to assess whether patients with ALS had higher risks of other neurodegenerative and psychiatric diseases before diagnosis. We included 3,648 patients with...

Journal: :Amyotrophic lateral sclerosis : official publication of the World Federation of Neurology Research Group on Motor Neuron Diseases 2010
Susan C Woolley Michele K York Dan H Moore Adriana M Strutt Jennifer Murphy Paul E Schulz Jonathan S Katz

Up to half of patients with ALS develop cognitive impairment during the course of the illness. Despite this, there is no simple tool for screening patients in the clinical setting. This study examines the sensitivity, specificity and accuracy of the ALS Cognitive Behavioral Screen (ALS-CBS). We administered the measure to 112 ALS patients, including 31 who also underwent comprehensive neuropsyc...

Journal: :Science translational medicine 2012
Naohiro Egawa Shiho Kitaoka Kayoko Tsukita Motoko Naitoh Kazutoshi Takahashi Takuya Yamamoto Fumihiko Adachi Takayuki Kondo Keisuke Okita Isao Asaka Takashi Aoi Akira Watanabe Yasuhiro Yamada Asuka Morizane Jun Takahashi Takashi Ayaki Hidefumi Ito Katsuhiro Yoshikawa Satoko Yamawaki Shigehiko Suzuki Dai Watanabe Hiroyuki Hioki Takeshi Kaneko Kouki Makioka Koichi Okamoto Hiroshi Takuma Akira Tamaoka Kazuko Hasegawa Takashi Nonaka Masato Hasegawa Akihiro Kawata Minoru Yoshida Tatsutoshi Nakahata Ryosuke Takahashi Maria C N Marchetto Fred H Gage Shinya Yamanaka Haruhisa Inoue

Amyotrophic lateral sclerosis (ALS) is a late-onset, fatal disorder in which the motor neurons degenerate. The discovery of new drugs for treating ALS has been hampered by a lack of access to motor neurons from ALS patients and appropriate disease models. We generate motor neurons from induced pluripotent stem cells (iPSCs) from familial ALS patients, who carry mutations in Tar DNA binding prot...

Journal: :Archives of neurology 2008
Agathe Paubel Jeremy Violette Maïté Amy Julien Praline Vincent Meininger William Camu Philippe Corcia Christian R Andres Patrick Vourc'h

BACKGROUND Mutations in the angiogenin gene, ANG, have been associated recently with familial and sporadic forms of amyotrophic lateral sclerosis (ALS). However, the cellular and molecular mechanisms that link ANG, a multidomain protein, to ALS are still unknown. OBJECTIVE To assess the frequency of ANG gene mutations in 855 French patients with sporadic ALS. DESIGN We analyzed by direct se...

Journal: :Journal of neuropathology and experimental neurology 2014
Leeanne McGurk Virginia M Lee John Q Trojanowksi Vivianna M Van Deerlin Edward B Lee Nancy M Bonini

Amyotrophic lateral sclerosis (ALS) is an adult-onset motor neuron disease in which the loss of spinal cord motor neurons leads to paralysis and death within a few years of clinical disease onset. In almost all cases of ALS, transactive response DNA binding protein of 43 kDa (TDP-43) forms cytoplasmic neuronal inclusions. A second causative gene for a subset of ALS is fused in sarcoma, an RNA b...

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