The McCune Albright syndrome is seldom encountered and rarely reported in dental literature. It represents a special category of polyostic fibrous displasia associated with skin pigmentation and endocrine disturbances. We describe the case of a 9-year-old boy with the McCune Albright syndrome, who was treated for a mandibular osteolytic lesion.

The alien hand syndrome is a deeply puzzling phenomenon in which brain-damaged patients experience their limb performing seemingly purposeful acts without their intention. Furthermore, the limb may interfere with the actions of their normal limb. We report a case of alien hand syndrome following a left medial frontal and corpus callosum ischemic lesion. From our clinical observations and the pa...

This clinical report describes the treatment and long-term follow-up of a patient with Sjogren's syndrome treated with osseointegrated implants and a mandibular fixed complete denture. The implants and prosthesis have remained stable and functional for 13 years. Implant treatment may, therefore, offer a viable long-term treatment alternative for patients with Sjogren's syndrome.

Normal craniofacial and dental growth and development is dependent on growth hormone (GH) and insulin-like growth factor I (IGF-I). Deficiencies of either during childhood cause diminished growth of the maxilla and (to a greater degree) the mandible. Dental development/eruption also is compromised. Conversely, excessive GH/insulin-like growth factor I causes overgrowth, with the mandible again ...

Port-wine stain is a vascular malformation characterized pathologically by ectasia of superficial dermal capillaris and clinically by persistent macular erythema. The association of a port-wine stain on a limb with soft tissue swelling, with or without bony overgrowth, is termed klippel-Trenaunay syndrome. Phakomatosis pigmento-vascularis is a combination of port-wine stain and cutaneous ...

Among the congenital otocephalic syndromes, the term "first and second branchial arch syndrome" designates, in the United States, a characteristic congenital malformation which is usually unilateral but occasionally bilateral. In the German literature, the deformity has been termed "dysostosis otomandibularis". Caronni (1971) has coined the term "auriculobranchiogenic dysplasia". Stark and Saun...

Ehlers-Danlos syndrome is a rare hereditary disease of the connective tissue which can present oral manifestations. A brief history of the disease is presented along with the epidemiology and characteristics of the 8 main phenotypes of the syndrome. The article also describes the case of a 12-year-old patient presenting with hypermobility of the temporo-mandibular joint and capillary fragility,...

OBJECTIVES In the first place, to evaluate skeletal changes of the maxilla and mandible induced by surgical-orthodontic correction of malocclusions class III with long-face syndrome and secondly, to analyze the stability of these skeletal changes in the long term (more than 6 years). DESIGN OF STUDY A retrospective, unicentric and longitudinal study of 19 patients who had undergone surgical a...

A44-year-oldwoman,with recurrent pancreatic cancer after a Whipple procedure, presented with afferent limb syndrome that manifested as sepsis secondary to cholangitis thought to be due to obstruction of the Roux limb by tumor recurrence. Endoscopy revealed an obstruction of the afferent limb (●" Fig.1) that could not be traversed with an endoscope or a guidewire under fluoroscopy. A dilated loo...