نتایج جستجو برای: ivs4

تعداد نتایج: 128  

Journal: :Brazilian journal of medical and biological research = Revista brasileira de pesquisas medicas e biologicas 2005
E B Tagliarini J G Assumpção M R Scolfaro M P de Mello A T Maciel-Guerra G Guerra Júnior C Hackel

The WT1 transcription factor regulates SRY expression during the initial steps of the sex determination process in humans, activating a gene cascade leading to testis differentiation. In addition to causing Wilms' tumor, mutations in WT1 are often responsible for urogenital defects in men, while SRY mutations are mainly related to 46,XY pure gonadal dysgenesis. In order to evaluate their role i...

Journal: :European Journal of Echocardiography 2023

Abstract Funding Acknowledgements Type of funding sources: None. Background Fabry disease (FD) is an X-linked lysosomal storage disorder due to a deficiency/absence alfa-galattosidase A enzyme activity. More than 1000 GLA gene mutations have been identified be causative classical or late-onset clinical phenotype. Cardiac variants (p.N215S, p.F113L and IVS4+919G>A) cause predominant cardi...

Journal: :genetics in the 3rd millennium 0
آنا عیسائیان anna isaian 1- department of pediatrics, children's medical center, tehran university of medical sciences, tehran, iran 2- national institute of genetic engineering and biotechnology, tehran, iran ناتالیا و.بوگدانووا natalia v. bogdanova gynaecology research unit, medical school of hannover, hannover, germany مسعود هوشمند masoud houshmand national institute of genetic engineering and biotechnology, tehran, iran مسعود موحدی masoud movahadi department of pediatrics, children's medical center, tehran university of medical sciences, tehran, iran اصغر آقا محمدی asghar agamohammadi 1- department of pediatrics, children's medical center, tehran university of medical sciences, tehran, iran نیما رضایی nima rezaei 1- department of pediatrics, children's medical center, tehran university of medical sciences, tehran, iran لیدا عطارد

ataxia telangiectasia (at) is an autosomal recessive multi-system disorder, characterized by variable immunodeficiency, progressive neurodegeneration, occulocutaneous telangiectasia, and increased susceptibility to malignancies. this study was designed to study the role of pro-apoptotic bak, bax, nbk/bik genes in a group of patients with at to elucidate the possible role of these genes in progr...

2007
Liezl Bloem SJ van Rensburg

DECLARATION I, the undersigned, hereby declare that the work contained in this thesis is my own original work and that I have not previously in its entirety or in part submitted it at any university for a degree. SUMMARY Multiple sclerosis (MS) is a disease that causes neurological dysfunction. Studies attempting to elucidate the role of genes in MS development may aid efforts to control the da...

2008
Jose A. Aragon-Martin Robert Ritch Jeffrey Liebmann Colm O’Brien Karima Blaaow Franco Mercieca Anthony Spiteri Caroline J. Cobb Karim F. Damji Ahti Tarkkanen Tayebeh Rezaie Anne H. Child Mansoor Sarfarazi

PURPOSE To evaluate genetic susceptibility of lysyl oxidase-like 1 (LOXL1) gene polymorphisms to exfoliation syndrome (XFS) and exfoliation glaucoma (XFG) in a case-control cohort of American and European patients. METHODS DNA from a total of 620 individuals including 287 exfoliation patients and 333 healthy control subjects were extracted by standard methods. Three single nucleotide polymorp...

Journal: :Blood 2003
Akiko Shimamura Alan D D'Andrea

Fanconi anemia (FA) is a rare autosomal recessive disease characterized by progressive bone marrow failure, congenital anomalies, and predisposition to cancer. At least 8 complementation groups for FA are known (A, B, C, D1, D2, E, F, G), and 7 FA genes have been cloned. FA cells are highly sensitive to the DNA crosslinking agents, mitomycin C (MMC) or diepoxybutane (DEB), thus providing the ba...

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