Congenital hearing loss has been documented to occur in 1 of 1000 live births, with over half of these cases predicted to be hereditary in nature. 2 Most hereditary hearing loss is inherited in a recessive manner, accounting for approximately 85% of non-syndromic hearing loss (NSHL). Deafness is an extremely genetically heterogeneous disorder, shown by the fact that 33 loci for recessive NSHL a...

Introduction: Children learn to communicate by hearing sounds. If there is hearing loss, the cognitive and speaking abilities and language learning will deteriorate. Early detection and intervention are important factors in the successful treatment of hearing loss in children. Hearing loss (HL) is divided into two main groups: conductive hearing loss (CHL) and sensorineural hearing loss (SNHL)...

conclusions the assr can accurately predict the degree and configuration of hearing loss and discriminate the normal hearing from mild or moderate hearing loss and mild from moderate hearing loss, except for 500 hz. the air-conducted assr could not define the type of hearing loss. results the assr accurately estimates the behavioral thresholds as well as flat and sloping configurations. there w...

A patient with Fuch's corneal dystrophy, sensorineural hearing loss, diabetes, cardiac conduction defects, ataxia, and hyperreflexia is described. Analysis of lymphocyte mitochondrial DNA showed missense mutations usually associated with Leber's hereditary optic neuropathy. The occurrence of Fuch's dystrophy in this patient and the biology of corneal endothelial cells suggest that mitochondrial...

Sertraline hydrochloride (Zoloft-Roeris Division, Pfizer Incorporated, New York) is an antidepressant medication that has numerous side effects, including dizziness, nausea, and tinnitus, documented during the period of medication . This presentation reports on Zoloftinduced unilateral tinnitus that resulted from withdrawal of the medication in a male patient with bilateral hereditary sensory h...

Hereditary hearing loss is a clinically and genetically heterogeneous disorder. More than 80 genes have been implicated to date, and with the advent of targeted genomic enrichment and massively parallel sequencing (TGE+MPS) the rate of novel deafness-gene identification has accelerated. Here we report a family segregating post-lingual progressive autosomal dominant non-syndromic hearing loss (A...

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introduction: hearing loss after surgery is reported rarely. its prevalence rate is different and reported to be between 3-92%. hearing loss is often subclinical and not diagnosed without audiometry. the aim of this study was to determine rate of hearing changes after spinal anesthesia in patients undergoing surgery with spinal anesthesia. methods: in this descriptive study, forty male patients...

introduction: occupational exposure to excessive noise is commonly encountered in a large number of industries in iran. this study evaluated the hearing threshold and hearing loss in meybod tile factory workers. methods: this cross-sectional study included 371 tile factoryworkers during summer and autumn of 2005. current noise exposure was estimated using sound level meter .a specially formatte...

introduction: otosclerosis one of the most common causes of conductive hearing loss is more common in females and in their middle ages. it is usually a bilateral and progressive disease. surgical operation is suggested as the exclusive management of otosclerosis. this study aims to evaluate the hearing results after stapedectomy in otosclerotic patients in ahwaz. materials and methods:  in this...