نتایج جستجو برای: col6a1

تعداد نتایج: 128  

2009
Jung Hwan Kim Min Ki Jee So Young Lee Tae Hee Han Bong Sun Kim Kyung Sun Kang Soo Kyung Kang

BACKGROUND To clarify the role of the POU domain transcription factor Oct4 in Adipose Tissue Stromal Cells (ATSCs), we investigated the regulation of Oct4 expression and other embryonic genes in fully differentiated cells, in addition to identifying expression at the gene and protein levels. The ATSCs and several immature cells were routinely expressing Oct4 protein before and after differentia...

2017
Wen-Chen Liang Xia Tian Chung-Yee Yuo Wan-Zi Chen Tsu-Min Kan Yi-Ning Su Ichizo Nishino Lee-Jun C. Wong Yuh-Jyh Jong

PURPOSE Congenital muscular dystrophy (CMD) is a heterogeneous disease entity. The detailed clinical manifestation and causative gene for each subgroup of CMD are quite variable. This study aims to analyze the phenotypes and genotypes of Taiwanese patients with CMD as the epidemiology of CMD varies among populations and has been scantly described in Asia. METHODS A total of 48 patients suspec...

2012
Jiyoung Park Philipp E. Scherer

Commentary on: Adipocyte-derived endotrophin promotes malignant tumor progression Collagen VI (COL6, encoded by the COL6A1, COL6A2, and COL6A3 genes) is an extracellular matrix protein that forms a microfilamentous network in various connective tissues, including skeletal muscle, cartilage, skin and adipose tissue. Among the various tissues, adipose tissue is by far the most abundant source of ...

2009
Andrea L. Vincent David M. Markie Betina De Karolyi Catherine E. Wheeldon Dipika V. Patel Christina N. Grupcheva Charles N.J. McGhee

PURPOSE With advances in phenotyping tools and availability of molecular characterization, an increasing number of phenotypically and genotypically diverse inherited corneal dystrophies are described. We aimed to determine the underlying causative genetic mechanism in a three-generation pedigree affected with a unique anterior membrane corneal dystrophy characterized by early onset recurrent co...

2017
Elizabeth Harris Ana Topf Rita Barresi Judith Hudson Helen Powell James Tellez Debbie Hicks Anna Porter Marta Bertoli Teresinha Evangelista Chiara Marini-Betollo Ólafur Magnússon Monkol Lek Daniel MacArthur Kate Bushby Hanns Lochmüller Volker Straub

BACKGROUND Limb girdle muscular dystrophies are a group of rare and genetically heterogeneous diseases that share proximal weakness as a common feature; however they are often lacking very specific phenotypic features to allow an accurate differential diagnosis based on the clinical signs only, limiting the diagnostic rate using phenotype driven genetic testing. Next generation sequencing provi...

Journal: :Clinical chemistry 2007
Attie T J I Go Allerdien Visser Monique A M Mulders Marinus A Blankenstein John M G van Vugt Cees B M Oudejans

To the Editor: For noninvasive prenatal diagnosis, markers that directly reflect changes in chromosome dosage are preferred over indirect markers that are associated with epiphenomena (1, 2). The RNA:single-nucleotide polymorphism (SNP) allelic ratio strategy was described recently as a means to directly assess fetal chromosome dosage in maternal plasma (2). Quantitive comparison of the allelic...

2011
Hong Gao Michael R. Frost John T. Siegwart Thomas T. Norton

PURPOSE To increase our understanding of the mechanisms that remodel the sclera during the development of lens-induced myopia, when the sclera responds to putative "go" signals of retinal origin, and during recovery from lens-induced myopia, when the sclera responds to retinally-derived "stop" signals. METHODS Seven groups of tree shrews were used to examine mRNA levels during minus lens comp...

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