نتایج جستجو برای: chronic granulomatous disease cgd

تعداد نتایج: 1773487  

Journal: :The Journal of clinical investigation 1969
D G Nathan R L Baehner D K Weaver

The leukocytes of patients with chronic granulomatous disease (CGD) may be identified by their failure to reduce Nitro Blue Tetrazolium (NBT) during phagocytosis. This reaction, normally detected in the phagocytic vacuole, is absent or delayed in CGD monocytes and eosinophils as well as in neutrophils, even though sonicates of normal and CGD leukocytes contain equal activities of a cyanide inse...

Journal: :iranian journal of allergy, asthma and immunology 0
monireh mohsenzadegan department of immunology, school of public health, tehran university of medical sciences, tehran, iran. fahimeh fattahi immunology, asthma and allergy research institute, tehran university of medical sciences, tehran, iran. fatemeh fattahi immunology, asthma and allergy research institute, tehran university of medical sciences, tehran, iran and department of pathology and medical biology, university medical center groningen, university of groningen, groningen, the netherlands. abbas mirshafiey department of immunology, school of public health, tehran university of medical sciences, tehran, iran. mohammad reza fazlollahi immunology, asthma and allergy research institute, tehran university of medical sciences, tehran, iran. fariba naderi beni department of immunology, school of public health, tehran university of medical sciences, tehran, iran.

chronic  granulomatous  disease (cgd)  is a rare primary immunodeficiency disorder characterized by a greatly increased susceptibility to severe fungal and bacterial infections caused  by  defects  in  nadph   oxidase  of  phagocytic  cells. we  aimed  to  investigate immunophenotype alterations of naïve and memory b cells and b1a cells in peripheral whole blood from iranian patients with cgd. ...

Journal: :Infection and immunity 1999
D P Speert B Steen K Halsey E Kwan

Burkholderia cepacia is an opportunistic pathogen that causes severe systemic infections in patients with chronic granulomatous disease (CGD) or with cystic fibrosis (CF), but its mechanisms of virulence are poorly understood. We developed a murine model of systemic infection in wild-type (WT) and gamma interferon knockout (GKO) BALB/c mice to facilitate dissection of components of pathogenicit...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2014
Antonella de Luca Sanne P Smeekens Andrea Casagrande Rossana Iannitti Kara L Conway Mark S Gresnigt Jakob Begun Theo S Plantinga Leo A B Joosten Jos W M van der Meer Georgios Chamilos Mihai G Netea Ramnik J Xavier Charles A Dinarello Luigina Romani Frank L van de Veerdonk

Patients with chronic granulomatous disease (CGD) have a mutated NADPH complex resulting in defective production of reactive oxygen species; these patients can develop severe colitis and are highly susceptible to invasive fungal infection. In NADPH oxidase-deficient mice, autophagy is defective but inflammasome activation is present despite lack of reactive oxygen species production. However, w...

Journal: :Blood 1999
M Kaneda H Sakuraba A Ohtake A Nishida C Kiryu K Kakinuma

Chronic granulomatous disease (CGD) is a disorder of host defense due to genetic defects of the superoxide (O2-) generating NADPH oxidase in phagocytes. A membrane-bound cytochrome b558, a heterodimer consisting of gp91-phox and p22-phox, is a critical component of the oxidase. The X-linked form of the disease is due to defects in the gp91-phox gene. We report here biochemical and genetic analy...

2003
Richard T. Kenney

The genetic defect in the p67Pk-deficient form of chronic granulomatous disease (CGD) follows an autosomal recessive pattern of inheritance. When genomic DNA from normal individuals is digested with Hindlll and probed with p67p"''x cDNA an allelic restriction fragment length polymorphism (RFLP) of 4.0 kb or 2.3 kb is detected. We cloned and characterized the p67Pk gene using the cDNA and sequen...

2013
J. F. Moreau John A. Ozolek P. Ling Lin Todd D. Green Elaine A. Cassidy Veena L. Venkat Andrew R. Buchert

Chronic granulomatous disease (CGD) is a rare inherited immunodeficiency syndrome that results from abnormal nicotinamide adenine dinucleotide phosphate (NADPH) oxidase function. This defect leads to recurrent catalase-positive bacterial and fungal infections as well as associated granuloma formation. We review the case of a 2-year-old boy who presented with ascites and fever of an unknown orig...

2017
Roxane Labrosse Jane Abou-Diab Annaliesse Blincoe Guilhem Cros Thuy Mai Luu Colette Deslandres Martha Dirks Laura Fazilleau Philippe Ovetchkine Pierre Teira Françoise LeDeist Isabel Fernandez Fabien Touzot Helene Decaluwe Ugur Halac Elie Haddad

Chronic granulomatous disease (CGD) is a rare primary immune deficiency caused by mutations in genes coding for components of the nicotinamide adenine dinucleotide phosphate oxidase, characterized by severe and recurrent bacterial and fungal infections, together with inflammatory complications. Dysregulation of inflammatory responses are often present in this disease and may lead to granulomato...

Journal: :Allergologia et immunopathologia 2014
L Berrón-Ruiz A Morín-Contreras V Cano-García M A Yamazaki-Nakashimada H Gómez-Tello M E Vargas-Camaño R Canseco-Raymundo F Saracho-Weber D Pietropaolo-Cienfuegos B Del Río-Navarro T Staines-Boone F Espinosa-Rosales A González-Del Ángel M M Saenz-de-Ocaris D Pacheco-Rosas S Espinosa-Padilla L Santos-Argumedo L Blancas-Galicia

BACKGROUND There are two inheritance patterns, the X-linked recessive (XL) pattern and the autosomal recessive pattern. There is no information on the predominant inheritance pattern of male patients with chronic granulomatous disease (CGD) in Mexico. OBJECTIVE The aim of this study was to determine the inheritance pattern in a cohort of Mexican male patients with CGD by means of the detectio...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید