Diphallia is a very rare congenital anomalies occurs 1: 5-6 Million live birth. Associated like imperforate anus, vertebral deformities, double bladder, exstrophy of the cloacae, and duplication recto sigmoid may in association with this. Amongst all anorectal malformations common anomaly that can occur diphallia. Here we are presenting neonate functional penis, partial scrotal dysraphism, high...

Background: Bladder exstrophy is a challenge to every surgeon in the world but it more challenging developing world. The condition highly varied nature and so are procedures. Though rare associated with severe disability not be able have continence of urine affect normal reproduction. Methods: We retrospectively retrieved documents from hospital records Result: describe 29 cases extrophy where ...

Heiko Reutter,* Lihong Qi, John P. Gearhart, Thomas Boemers, Anne-Karoline Ebert, Wolfgang Rösch, Michael Ludwig, and Simeon A. Boyadjiev Department of Human Genetics, University of Bonn, Bonn, Germany Rowe Program in Human Genetics, Department of Public Health Sciences, University of California—Davis, Davis, California Department of Urology, The Johns Hopkins Hospital, Baltimore, Maryland Depa...

Among the developmental anomalies seen in children, few has as broad a spectrum as the exstrophy-epispadias complex which encompasses numerous abnormalities arising in the hind-end of the embryo. Table 1, the scheme proposed by Marshal and Muecke, depicts the developmental relationships of the variations within the complex. One can readily appreciate the multifaceted nature of a syndrome which ...

Mitrofanoff appendicovesicostomy has been the method of choice for dealing with urinary incontinence. However, there may be some cases where some alternate conduits have to be used. Yang-Monti ileovesicostomy is an alternative to Mitrofanoff appendicovesicostomy. Three boys who underwent successful Yang-Monti continent ileovesicostomy are reported in this manuscript. In the first case, Mitrofan...

OBJECTIVE To evaluate the emotional and behavioral functioning of children with bladder exstrophy-epispadias complex (BEEC), taking into account developmental and gender considerations. This study also sought to overcome methodological limitations of previous studies evaluating psychological well-being of children with BEEC. METHODS Eighty-six children were consecutively evaluated using the p...

Isolated female epispadias without bladder exstrophy is a rare congenital anomaly affecting 1 in 484,000 females. The presenting features of female epispadias are urinary incontinence and abnormal anatomical features. A 6-year-old girl presented with primary urinary incontinence who on physical examination had a bifid clitoris and labia minora. The vagina and hymen were normal. Voiding cystoure...

Human bladder exstrophy-epispadias complex (BEEC) comprises a spectrum of urogenital anomalies in which part or all of the distal urinary tract fails to close. Several lines of evidence implicate genetic factors in the formation of BEEC. Among them a murine p63+/+ knockout model showed the full picture of classic exstrophy of the bladder and other urogenital defects within the BEEC spectrum. Th...