نتایج جستجو برای: autosomal dominant polycystic kidney disease adpkd

تعداد نتایج: 1745684  

2014
GOPALA K. RANGAN BRIAN J. NANKIVELL

A utosomal dominant polycystic kidney disease (ADPKD) is a genetic condition characterised by the formation of multiple fluid-filled renal cysts and kidney enlargement. Potential complications of ADPKD include adult-onset end-stage kidney disease, early-onset hypertension and nephrolithiasis. ADPKD is also associated with systemic conditions including intracranial cerebral aneurysm and polycyst...

Journal: :World journal of gastroenterology 2007
Robert T Russell C Wright Pinson

Adult polycystic liver disease (PCLD) is an autosomal dominant condition commonly associated with autosomal dominant polycystic kidney disease (ADPKD). However in the last decade, it has been recognized that there is a distinct form of autosomal dominant PCLD that arises without concomitant ADPKD. Early knowledge of the pathogenesis was gained from the study of hepatic cysts in patients with AD...

2017
Melissa A. Cadnapaphornchai

Autosomal dominant polycystic kidney disease (ADPKD) is the most common hereditary kidney disease and is associated with concerning long-term implications for kidney function and cardiovascular health. Early intervention is needed in order to mitigate these long-term complications. Herein, we review important findings from recent clinical trials in ADPKD and their relevance to affected children...

2011
VV Sainaresh SH Jain HV Patel PR Shah AV Vanikar HL Trivedi

Urinary tract infection (UTI) is the most common infection contracted by renal allograft recipients. In patients of autosomal dominant polycystic kidney disease (ADPKD), cyst infection presents a complex diagnostic and therapeutic challenge especially in the post transplant period. Accurate diagnosis forms the cornerstone in salvaging the graft from potentially catastrophic outcome. We describe...

Journal: :Iranian journal of kidney diseases 2012
Shokoufeh Savaj Mahmoud Parvin Javad Savoj

Autosomal dominant polycystic kidney disease (ADPKD) with nephrotic syndrome is a rare coincidence. Among 19 reported cases since 1972, focal glomerulosclerosis is the dominant reported pathology. Here, we report the 6th case of focal segmental glomerulosclerosis with ADPKD. A 29-year-old man with a history of APCDK presented with massive proteinuria. He had a history of concurrent leptospirosi...

2017
Sachin Hajarnis Ronak Lakhia Matanel Yheskel Darren Williams Mehran Sorourian Xueqing Liu Karam Aboudehen Shanrong Zhang Kara Kersjes Ryan Galasso Jian Li Vivek Kaimal Steven Lockton Scott Davis Andrea Flaten Joshua A Johnson William L Holland Christine M Kusminski Philipp E Scherer Peter C Harris Marie Trudel Darren P Wallace Peter Igarashi Edmund C Lee John R Androsavich Vishal Patel

Autosomal dominant polycystic kidney disease (ADPKD) is the most frequent genetic cause of renal failure. Here we identify miR-17 as a target for the treatment of ADPKD. We report that miR-17 is induced in kidney cysts of mouse and human ADPKD. Genetic deletion of the miR-17∼92 cluster inhibits cyst proliferation and PKD progression in four orthologous, including two long-lived, mouse models of...

2014
Maria Wanic-Kossowska Bartlomiej Posnik Mikolaj Kobelski Elzbieta Pawliczak Krzysztof Pawlaczyk Krzysztof Hoppe Krzysztof Schwermer Dorota Sikorska

Autosomal dominant polycystic kidney disease (ADPKD) is one of the most frequently occurring autosomal diseases inherited in the dominant manner. Due to this, lesions in the cardiovascular system of ADPKD patients have caught the attention of clinical investigators worldwide. The aim of the study was to analyse cardiovascular complications in ADPKD patients with a focus on left ventricular hype...

Journal: :Polish journal of pathology : official journal of the Polish Society of Pathologists 2013
S Konosu-Fukaya Y Nakamura F Fujishima A Kasajima Y Takahashi K Joh Y Ikeda N Ioritani M Watanabe H Sasano

We herein report two rare cases of bilateral renal neoplasms associated with autosomal dominant polycystic kidney disease (ADPKD). Case 1: Bilateral nephrectomy was performed on bilateral renal masses in a 58-year-old man with ADPKD. Case 2: Bilateral nephrectomy was performed on bilateral renal masses in a 32-year-old man with clinically suspected ADPKD. In case 1, angiomyolipoma (AML) and pap...

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