نتایج جستجو برای: ژن pah

تعداد نتایج: 23292  

Journal: :American journal of physiology. Lung cellular and molecular physiology 2014
Tim Lahm Rubin M Tuder Irina Petrache

Pulmonary arterial hypertension (PAH) is a devastating and progressive disease with marked morbidity and mortality. Even though being female represents one of the most powerful risk factors for PAH, multiple questions about the underlying mechanisms remain, and two "estrogen paradoxes" in PAH exist. First, it is puzzling why estrogens have been found to be protective in various animal models of...

2013
Sébastien Renard Roxane Paulin Sandra Breuils-Bonnet Serge Simard Philippe Pibarot Sébastien Bonnet Steeve Provencher

Provirus integration site for Moloney murine leukemia virus (Pim-1) is an oncoprotein overexpressed in lungs from pulmonary arterial hypertension (PAH) patients and involved in cell proliferation via the activation of the NFAT/STAT3 signaling pathway. We hypothesized that Pim-1 plasma levels would predict the presence of PAH and correlate with disease severity. Pim-1 plasma levels were measured...

2011
Paulina Mocchiutti María V. Galván María C. Inalbon Miguel A. Zanuttini

Polyelectrolytes containing amine functional groups such as PAH (poly(allylamine hydrochloride)) can be useful, under certain conditions, for improving paper strength. In this work, the charge density of PAH was determined at different pH and ionic strengths; PAH adsorption onto the cellulosic fibers was characterized, and the effects of low PAH dosage on the papermaking properties were evaluat...

Journal: :The Journal of chemical physics 2015
Yang Li Xingchen Tu Hao Wang Stefano Sanvito Shimin Hou

The electronic efficiency and binding energy of contacts formed between graphene electrodes and poly-aromatic hydrocarbon (PAH) anchoring groups have been investigated by the non-equilibrium Green's function formalism combined with density functional theory. Our calculations show that PAH molecules always bind in the interior and at the edge of graphene in the AB stacking manner, and that the b...

Journal: :Circulation 2016
Steven Hsu Brian A Houston Emmanouil Tampakakis Anita C Bacher Parker S Rhodes Stephen C Mathai Rachel L Damico Todd M Kolb Laura K Hummers Ami A Shah Zsuzsanna McMahan Celia P Corona-Villalobos Stefan L Zimmerman Fredrick M Wigley Paul M Hassoun David A Kass Ryan J Tedford

BACKGROUND Right ventricular (RV) functional reserve affects functional capacity and prognosis in patients with pulmonary arterial hypertension (PAH). PAH associated with systemic sclerosis (SSc-PAH) has a substantially worse prognosis than idiopathic PAH (IPAH), even though many measures of resting RV function and pulmonary vascular load are similar. We therefore tested the hypothesis that RV ...

2016
Sébastien Sanges Cécile M. Yelnik Olivier Sitbon Olivier Benveniste Kuberaka Mariampillai Mathilde Phillips-Houlbracq Christophe Pison Christophe Deligny Jocelyn Inamo Vincent Cottin Luc Mouthon David Launay Marc Lambert Pierre-Yves Hatron Laurence Rottat Marc Humbert Eric Hachulla

Occurrence of pulmonary arterial hypertension (PAH) in idiopathic inflammatory myopathies (IIMs) without extensive interstitial lung disease (ILD) has rarely been described in the medical literature. This study aimed to report all cases with association of PAH and IIM in the French Pulmonary Hypertension (PH) Registry, to identify IIM features associated with the presence of PAH, and to describ...

2017
Heon-Woo Lee Suk-Won Jin

Pulmonary artery hypertension (PAH) is a rare lung disorder in which the arteries that carry blood from the heart to the lungs progressively narrow down, making it difficult for blood to flow through the vessels. In many cases, PAH leads to right ventricular failure. The recent estimate of 1-, 3-, and 5-year survival rates from the time of diagnosis were estimated to be 87.7%, 72.1% , and 60.3%...

Journal: :European heart journal 2014
Alessandra Manes Massimiliano Palazzini Enri Leci Maria L Bacchi Reggiani Angelo Branzi Nazzareno Galiè

AIMS This study compared the clinical, functional, and haemodynamic characteristics and current era survival of subgroups of patients with pulmonary arterial hypertension associated with congenital heart disease (PAH-CHD): Eisenmenger syndrome (ES); PAH-CHD associated with systemic-to-pulmonary shunts (SPs); PAH with small defects (SDs); and PAH after defect correction (CDs). METHODS AND RESU...

Journal: :Circulation 2013
Silvia Rain M Louis Handoko Pia Trip C Tji-Joong Gan Nico Westerhof Ger J Stienen Walter J Paulus Coen A C Ottenheijm J Tim Marcus Peter Dorfmüller Christophe Guignabert Marc Humbert Peter Macdonald Cris Dos Remedios Piet E Postmus Chandra Saripalli Carlos G Hidalgo Henk L Granzier Anton Vonk-Noordegraaf Jolanda van der Velden Frances S de Man

BACKGROUND The role of right ventricular (RV) diastolic stiffness in pulmonary arterial hypertension (PAH) is not well established. Therefore, we investigated the presence and possible underlying mechanisms of RV diastolic stiffness in PAH patients. METHODS AND RESULTS Single-beat RV pressure-volume analyses were performed in 21 PAH patients and 7 control subjects to study RV diastolic stiffn...

Journal: :Molecular and biochemical parasitology 2011
Lon-Fye Lye Song Ok Kang Joshua D Nosanchuk Arturo Casadevall Stephen M Beverley

Aromatic amino acid hydroxylases (AAAH) typically use tetrahydrobiopterin (H(4)B) as the cofactor. The protozoan parasite Leishmania major requires biopterin for growth and expresses strong salvage and regeneration systems to maintain H(4)B levels. Here we explored the consequences of genetic manipulation of the sole L. major phenylalanine hydroxylase (PAH) to explore whether it could account f...

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