نتایج جستجو برای: yq microdeletion

تعداد نتایج: 1741  

Journal: :European journal of medical genetics 2011
Christèle Dubourg Damien Sanlaville Martine Doco-Fenzy Cédric Le Caignec Chantal Missirian Sylvie Jaillard Caroline Schluth-Bolard Emilie Landais Odile Boute Nicole Philip Annick Toutain Albert David Patrick Edery Anne Moncla Dominique Martin-Coignard Catherine Vincent-Delorme Isabelle Mortemousque Bénédicte Duban-Bedu Sèverine Drunat Mylène Beri Jean Mosser Sylvie Odent Véronique David Joris Andrieux

Chromosome 17q21.31 microdeletion was one of the first genomic disorders identified by chromosome microarrays. We report here the clinical and molecular characterization of a new series of 14 French patients with this microdeletion syndrome. The most frequent clinical features were hypotonia, developmental delay and facial dysmorphism, but scaphocephaly, prenatal ischemic infarction and percept...

Journal: :Clinical endocrinology 2003
Paolo A Tomasi Robert Oates Laura Brown Giuseppe Delitala David C Page

OBJECTIVE The most frequent known genetic causes of severe oligospermia (< 5 million sperm/ml) or azoospermia in men are Klinefelter's syndrome (KS), and deletions in the Y chromosome long arm (Yq). We aimed to compare the function of the pituitary-testicular axis in patients with severe oligospermia or azoospermia, idiopathic or associated with Y chromosome deletions or Klinefelter's syndrome ...

Journal: :modares journal of medical sciences: pathobiology 2007
sara pouranvari mehrdad noruzinia aliakbar zinalou saeedreza ghafari masoud houshmand

objective: 22q11.2 chromosomal region is a hot spot for many cytogenetic rearrangements especially microdeletions which are responsible for digeorge and velocardiofacial syndromes. the most characteristic sign in these patients is congenital cardiac conotruncal anomalies. the gold standard diagnostic test for these microdeletions is fish (fluorescent in situ hybridization). however this diagnos...

2014
Ramaswamy Suganthi Vijayabhavanath Vijayakumaran Vijesh Nambiar Vandana Jahangir Fathima Ali Benazir

Spermatogenesis is an essential stage in human male gamete development, which is regulated by many Y chromosome specific genes. Most of these genes are centred in a specific region located on the long arm of the human Y chromosome known as the azoospermia factor region (AZF). Deletion events are common in Y chromosome because of its peculiar structural organization. Astonishingly, among the sev...

Journal: :Molecular syndromology 2012
M H Willemsen A T Vulto-van Silfhout W M Nillesen W M Wissink-Lindhout H van Bokhoven N Philip E M Berry-Kravis U Kini C M A van Ravenswaaij-Arts B Delle Chiaie A M M Innes G Houge T Kosonen K Cremer M Fannemel A Stray-Pedersen W Reardon J Ignatius K Lachlan C Mircher P T J M Helderman van den Enden M Mastebroek P E Cohn-Hokke H G Yntema S Drunat T Kleefstra

Kleefstra syndrome is characterized by the core phenotype of developmental delay/intellectual disability, (childhood) hypotonia and distinct facial features. The syndrome can be either caused by a microdeletion in chromosomal region 9q34.3 or by a mutation in the euchromatin histone methyltransferase 1 (EHMT1) gene. Since the early 1990s, 85 patients have been described, of which the majority h...

2016
Ehsan Yousefi-Razin Mohammad Javad Nasiri Mir Davood Omrani

BACKGROUND While multiple factors can contribute to male infertility, genetic factors, such as chromosomal disorders or Y-chromosome microdeletion, are responsible for about 10% of male infertility. Considering the role of Y-chromosome micro-deletions in men with oligozoospermia who volunteer for in vitro fertilization (IVF), the prevalence of such microdeletions in each particular community ne...

Journal: :Archives of general psychiatry 2001
S Eliez S E Antonarakis M A Morris S P Dahoun A L Reiss

BACKGROUND As children with velocardiofacial syndrome (VCFS) develop, they are at increased risk for psychopathology; one third will eventually develop schizophrenia. Because VCFS and the concomitant symptomatology result from a known genetic origin, the biological and behavioral characteristics of the syndrome provide an optimal framework for conceptualizing the associations among genes, brain...

Journal: :international journal of reproductive biomedicine 0
mohammad reza nowroozi keivan radkhah alireza ranjbaran saeed reza ghaffari mohammad ali sedighi gilani hamid gourabi

background: the sperm count and function may be affected by karyotype abnormalities or microdeletion in y chromosome. these genetic abnormalities can probably transmit to the children. objective: in this study, we tried to determine the frequency of karyotype abnormalities and y chromosome microdeletions in severe oligospermic or azoospermic men who fathered sons by icsi. materials and methods:...

Journal: :Journal of Histochemistry & Cytochemistry 2012

2014
Deborah Y Kwon Zhaolan Zhou

Despite genetic evidence implicating MBD5 as the only overlapping gene between various 2q23.1 microdeletions, the function of MBD5 and its causality to 2q23.1 microdeletion syndrome, a disorder characterized by developmental delay and autistic features, has yet to be determined. In this issue of EMBO Molecular Medicine, Camarena et al generate an Mbd5 genetrap mouse model and show for the first...

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