Ectodermal dysplasias (EDs)are a heterogenous group of hereditary disorders characterized by certain shared structural and functional abnormalities in tissues derived from the ectoderm [1]. They are characterized by deficient function of at least 2 ectodermal derivatives such as skin, hair, teeth and sweat glands. Although more than 170 different subtypes of ectodermal dysplasia have been ident...

The spontaneous assembly of aromatic cation-radicals (D(+)(*)()) with the parent donor (D) to afford the paramagnetic dimer (D)(2)(+)(*)() is accompanied by a dramatic color change. For example, spectral (UV-vis and ESR) and X-ray crystal structure analyses establish the molecular association of octamethylbiphenylene cation-radical with its neutral counterpart to produce the mixed-valence or di...

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Familial Florid cemento-osseous dysplasia is a very uncommon condition. Cemento-osseous dysplasia is totally asymptomatic in many cases, in those conditions, lesions are detected in a radiograph taken for other purposes. In this report, we describe a family in which mother and daughter exhibited clinical, radiographic, and histologic features of florid cemento-osseous dysplasia.

A family is described in which sometimes asymmetrical brachydactyly, with nail dysplasia of the involved fingers, has been transmitted through 6 generations affecting 6 males and 15 females. The thumbs and feet have been normal. This previously unreported condition is inherited as an autosomal disorder with full penetrance and variable expressivity, and causes only minor inconvenience.