نتایج جستجو برای: thalassemia majorcardiac abnormalitiestei

تعداد نتایج: 20990  

Journal: :Frontiers in Medicine 2023

Background Thalassemia is a common inherited hemoglobin disorder caused by deficiency of one or more globin subunits. Substitution variants and deletions in the HBB gene are major causes β-thalassemia, which large fragment rare difficult to be detected conventional polymerase chain reaction (PCR)-based methods. Case report In this study, we reported 26-year-old Han Chinese man, whose routine bl...

Journal: : 2023

Mục tiêu: Mô tả đặc điểm thiếu máu và quá tải sắt của bệnh nhân Thalassemia tại Viện Huyết học Truyền Trung ương giai đoạn 2020 – 2022. Đối tượng phương pháp: Nghiên cứu mô cắt ngang trên 3097 điều trị tâm Thalassemia, từ 01/2020 đến 03/2022. Kết quả: Nhóm β-Thalassemia thể nặng có nồng độ huyết sắc tố trung bình thấp nhất tỉ lệ rất cao nhất. Sự khác biệt về mức giữa các là ý nghĩa thống kê (p ...

Journal: :Black sea journal of health science 2022

Thalassemia minor carriage is one of the most common causes anemia in Mediterranean countries. This study aimed to investigate publications scientific journals on thalassemia minor, which an important health problem, especially The goal this was retrieve data from that were indexed Web Science (WoS; Thomson Reuters, New York, NY, USA) database. WOS Core Collection used comprehensive bibliometri...

2013
Min Lin Ying-Fang Wen Jiao-Ren Wu Qian Wang Lei Zheng Gui-Rong Liu Yue Huang Hui Yang Fen Lin Xiao-Fen Zhan Chun-Ping Lin Hui-Tian Yang Qiu-Qing Weng Fen-Ting Huang Yuan Wang Mei-Qiong Yao Hui-Zhou Chen Di-Hong Wu Jing-Bo Zeng Ri-Xin Zeng Hua Yang Gui-Cai Li Min Lu Juan-Juan Zhu Long-Xu Xie Jun-Li Wang Li-Ye Yang

BACKGROUND Hemoglobinopathies are the most common inherited diseases in southern China. However, there have been only a few epidemiological studies of hemoglobinopathies in Guangdong province. MATERIALS AND METHODS Peripheral blood samples were collected from 15299 "healthy" unrelated subjects of dominantly ethnic Hakka in the Meizhou region, on which hemoglobin electrophoresis and routine bl...

2003
CHRISTOPHILLE SKARMOUTSOU IOANNIS PAPASSOTIRIOU JOANNE TRAEGER-SYNODINOS HELENE STAMOU VASSILIOS LADIS ANNA METAXOTOU-MAVROMMATI ALEXANDRA STAMOULAKATOU EMMANUEL KANAVAKIS

631 Background and Objectives. Ferrokinetic studies and erythroid cell ultrastructural studies have indicated some degree of ineffective erythropoiesis in heterozygous β-thalassemia, although a wide case-to-case variation was observed. In this study we applied rapid biochemical and hematologic measurements to assess erythroid marrow activity (sTfR) and reticulocyte hemoglobin content (CHr) in i...

2016
Keith Quirolo Elliott Vichinsky

Each year, an estimated 300,000 infants are born with either of the two most common hemoglobinopathies: the sickle cell diseases or the thalassemias. These inherited diseases are the most prevalent monogenetic disorders worldwide. Sickle cell disease makes up 85% of the total infants, and thalassemias the remaining 15%. It is increasingly apparent that sickle cell disease and thalassemia have b...

2014
Anthony Haddad Paul Tyan Amr Radwan Naji Mallat Ali Taher

Beta-thalassemia is due to a defect in the synthesis of the beta-globin chains, leading to alpha/beta imbalance, ineffective erythropoiesis, and chronic anemia. The spectrum of thalassemias is wide, with one end comprising thalassemia minor, which consists of a mild hypochromic microcytic anemia with no obvious clinical manifestations, while on the other end is thalassemia major, characterized ...

2015
Abdolreza Sotoodeh Jahromi Karamatollah Rahmanian

PURPOSE Patients with beta thalassemia major are at increased risk for bacterial infections specially splenectomized patients. The aim of this study was to determine the anti-tetanus antibody concentration among patients with beta thalassemia major. MATERIALS AND METHODS The anti-tetanus antibody concentration was investigated in 224 patients with thalassemia major and 224 healthy subjects ma...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2009
A O'Donnell A Premawardhena M Arambepola R Samaranayake S J Allen T E A Peto C A Fisher J Cook P H Corran Nancy F Olivieri D J Weatherall

In many Asian populations, the commonest form of severe thalassemia results from the coinheritance of HbE and beta thalassemia. The management of this disease is particularly difficult because of its extreme clinical diversity; although some genetic and adaptive factors have been identified as phenotypic modifiers, the reasons remain unclear. Because the role of the environment in the course of...

Journal: :Collegium antropologicum 2009
Asena C Dogramaci Nazan Savas Mehmet A Bagriacik

Dermatoglyphs are cutaneous ridges on the fingers, palms, and soles, formed during early intrauterine life. During this period, and only then, genetic and environmental factors can influence their formation. Beta-thalassemia major is an genetic disease. The aim of the present work was to analyze dermatoglyphs traits in subjects with beta-thalassemia major and their thalassemia carrier parents. ...

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