IN 1938 Oppenheimer1 reported the first case of bilateral stenosis of the pulmonary main arteries diagnosed at autopsy. Since then several papers have been published describing clinical, cardiac catheterization, and angiocardiographic findings in both unilateral and bilateral stenosis of the pulmonary arteries.2-12 We are reporting cardiac catheterization and angiocardiographic findings in 12 p...

Dilatation of the pulmonary artery occurs frequently in cases of valvular pulmonary stenosis and is often called "poststenotic." We determined the diameter of the pulmonary artery angiocardio-graphically and compared this with the data obtained by heart catheterization in cases of pulmonary stenosis and of idiopathic dilatation of the pulmonary artery. Features are presented which constitute ar...

The diagnosis of primary pulmonary vein stenosis is often overlooked because its symptoms overlap lung diseases and pulmonary arterial hypertension. Its diagnosis may be difficult because the condition is progressive and associated with other defects. We present a case of pulmonary vein stenosis in a newborn with stenosis of the left-sided common pulmonary vein, diffuse hypoplasia of the superi...

Pulmonary hypertension frequently complicates mitral stenosis. Increased pulmonary artery pressure results from raised left atrial pressure, pulmonary arteriolar constriction, and obliterative changes in the pulmonary vascular bed, and usually responds to surgical relief of mitral stenosis. However, severe pulmonary hypertension may persist after surgical treatment of mitral stenosis. We descri...

Between January 1983 and December 1987, 62 patients underwent an arterial switch operation for transposition of the great arteries with ventricular septal defect or double outlet right or left ventricle. There were three hospital deaths (4.8%), and no deaths occurred in neonates (<1 month of age, n= 18). There were three late deaths, one due to coronary obstruction and two due to pulmonary vasc...

OBJECTIVE To evaluate the cardiovascular findings and clinical follow-up of patients with Williams-Beuren syndrome. METHODS We studied 20 patients (11 males, mean age at diagnosis: 5.9 years old), assessed for cardiovascular abnormalities with electrocardiography and Doppler echocardiography. Fluorescence in situ hybridization (FISH) was used to confirm the diagnosis of the syndrome. RESULT...

This report describes 3 cases of pulmonary stenosis in the recipient twin in twin-twin transfusion syndrome. Fetal echocardiography showed cardiomegaly, tricuspid valve regurgitation, and increased reverse flow in the inferior vena cava, as signs of congestive heart failure in all 3 cases. We diagnosed 2 cases of pulmonary stenosis by fetal echocardiography prenatally and confirmed our findings...

Reestablishment of aortic flow to the coronary vasculature is the optimal treatment for anomalous origin of the left coronary artery originating from the pulmonary artery (ALCA). We performed intraoperative transesophageal echocardiography (TEE) in five patients (median age 10 months; range 1.5-36 months) who underwent revascularization of the left coronary artery without coronary mobilization ...

BACKGROUND Congenital pulmonary valve stenosis and patent ductus arteriosus are common congenital heart defects in dogs. However, concurrence of atypical pulmonary valve stenosis and patent ductus arteriosus is uncommon. This report describes the anatomic, histopathologic, and echocardiographic features in a dog with concomitant pulmonary valve stenosis and patent ductus arteriosus with atypica...