نتایج جستجو برای: spondyloepiphyseal dysplasia

تعداد نتایج: 28617  

2012
E. Bozkurt

The purpose of this study was to investigate the effect of combining Real Experimentation (RE) With Virtual Experimentation (VE) on students’ conceptual understanding of photo electric effect. To achieve this, a pre–post comparison study design was used that involved 46 undergraduate students. Two groups were set up for this study. Participants in the control group used RE to learn photo electr...

Journal: :Paediatria Croatica 2021

Background: Schimke immuno-osseous dysplasia (SIOD, OMIM 242900) is a rare, autosomal recessive, pleiotropic disease caused by mutations in the SMARCAL1 gene. SIOD characterized triad of symptoms, i.e., progressive kidney due to focal segmen- tal glomerulosclerosis (FSGS), spondyloepiphyseal and T-cell immunodeficiency. Additionally, heterogeneous neurological symptoms are often observed course...

Journal: :The Journal of clinical investigation 2017
Adetutu T Egunsola Yangjin Bae Ming-Ming Jiang David S Liu Yuqing Chen-Evenson Terry Bertin Shan Chen James T Lu Lisette Nevarez Nurit Magal Annick Raas-Rothschild Eric C Swindell Daniel H Cohn Richard A Gibbs Philippe M Campeau Mordechai Shohat Brendan H Lee

Shohat-type spondyloepimetaphyseal dysplasia (SEMD) is a skeletal dysplasia that affects cartilage development. Similar skeletal disorders, such as spondyloepiphyseal dysplasias, are linked to mutations in type II collagen (COL2A1), but the causative gene in SEMD is not known. Here, we have performed whole-exome sequencing to identify a recurrent homozygous c.408+1G>A donor splice site loss-of-...

Journal: :The Kaohsiung journal of medical sciences 2013
Yu-Chih Lin Te-Fu Chan Chung-Sheng Lai Chi-Chun Chin Fan-Hao Chou Hui-Ju Lin

Clinical ethic situations in modern multiprofessional healthcare systems may involve different healthcare professions who work together for patient care. The undergraduate interprofessional education of clinical ethics would help to incubate healthcare students' ability of interprofessional collaboration in solving ethical problems. However, the impact from an interprofessional educational mode...

2016
Shingo Kitamura Yasuko Katayose Kyoko Nakazaki Yuki Motomura Kentaro Oba Ruri Katsunuma Yuri Terasawa Minori Enomoto Yoshiya Moriguchi Akiko Hida Kazuo Mishima

In this study, we hypothesized that dynamics of sleep time obtained over consecutive days of extended sleep in a laboratory reflect an individual's optimal sleep duration (OSD) and that the difference between OSD and habitual sleep duration (HSD) at home represents potential sleep debt (PSD). We found that OSD varies among individuals and PSD showed stronger correlation with subjective/objectiv...

Journal: :Orthopedics 2012
Kevin E Klingele Scott Stephens

Congenital knee dislocation is a rare anomaly associated with a variety of neuromuscular diseases and deformities. The etiology of this condition remains unclear, but it is usually associated with a variety of disorders, such as Larsen's syndrome, arthrogryposis, spondyloepiphyseal dysplasia, Ehlers-Danlos syndrome, Down syndrome, and Streeter's dysplasia. It is rarely an isolated entity, and 6...

2008
Thomas Lücke Lars Pape

A 17-year-old girl (height: 16 cm below the third percentile; weight 10 kg below the third percentile) was diagnosed with familial steroid-resistant nephrotic syndrome at the age of 6 years. A renal biopsy was performed at this time, which showed that all 16 glomeruli were normal by light microscopy. Neither steroid therapy, cyclosporine A nor ACE inhibitor therapy led to remission. The patient...

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