نتایج جستجو برای: myeloproliferative neoplasm

تعداد نتایج: 188264  

2017

The excess release of mediators can cause clinical features such as pruritus, flushing, nausea, vomiting, diarrhoea, abdominal pain, vascular instability and anaphylaxis. Also, complications may arise when mast cells accumulate in the skin, gastrointestinal tract, bone marrow, liver, spleen, and lymph nodes. [2] The clinical features of systemic mastocytosis are caused by accumulation of clonal...

2017

The excess release of mediators can cause clinical features such as pruritus, flushing, nausea, vomiting, diarrhoea, abdominal pain, vascular instability and anaphylaxis. Also, complications may arise when mast cells accumulate in the skin, gastrointestinal tract, bone marrow, liver, spleen, and lymph nodes. [2] The clinical features of systemic mastocytosis are caused by accumulation of clonal...

2017
M M Patnaik M M Timm R Vallapureddy T L Lasho R P Ketterling N Gangat M Shi A Tefferi E Solary K K Reichard D Jevremovic

Chronic myelomonocytic leukemia (CMML) is a myelodysplastic syndrome/myeloproliferative neoplasm (MDS/MPN) overlap syndrome characterized by peripheral blood monocytosis (absolute monocyte count/AMC ⩾ 1 × 10(9)/l, ⩾ 10% of the total white blood cell count) and an inherent risk for leukemic transformation. Monocytosis, however, is not pathognomic for CMML and can be associated with reactive and ...

2016
Monica Midha Marnie E. Rosenthal

While many cases of streptococcal infection are due to Lancefield groups A and B, there has been a rise in reported cases of infections due to group G streptococcus. We present a case of an individual with a hematologic malignancy who developed myositis secondary to group G streptococcus, with no clearly identifiable source of infection. The patient was managed with antibiotic therapy rather th...

Journal: :Blood 2016
Ilyas Chachoua Christian Pecquet Mira El-Khoury Harini Nivarthi Roxana-Irina Albu Caroline Marty Vitalina Gryshkova Jean-Philippe Defour Gaëlle Vertenoeil Anna Ngo Ann Koay Hana Raslova Pierre J Courtoy Meng Ling Choong Isabelle Plo William Vainchenker Robert Kralovics Stefan N Constantinescu

Mutations in the calreticulin gene (CALR) represented by deletions and insertions in exon 9 inducing a -1/+2 frameshift are associated with a significant fraction of myeloproliferative neoplasms (MPNs). The mechanisms by which CALR mutants induce MPN are unknown. Here, we show by transcriptional, proliferation, biochemical, and primary cell assays that the pathogenic CALR mutants specifically a...

2013
Steven W. Lane Ann Mullally

The myeloproliferative neoplasms (MPNs) are clonal disorders of hematopoiesis that arise as a result of aberrant activation of tyrosine kinases and result in the proliferation and accumulation of mature myeloid cells in the blood, bone marrow and spleen. The prototypical MPN, chronic myeloid leukemia (CML) is caused by constitutive activation of ABL kinase occurring as a result of the BCR-ABL f...

2017
Bing Li Robert Peter Gale Zefeng Xu Tiejun Qin Zhen Song Peihong Zhang Jie Bai Lei Zhang Yue Zhang Jinqin Liu Gang Huang Zhijian Xiao

We studied non-driver mutations in 62 subjects with myeloproliferative neoplasm (MPN)-associated myelofibrosis upon diagnosis, including 45 subjects with primary myelofibrosis (PMF) and 17 with post-polycythemia vera or post-essential thrombocythemia myelofibrosis (post-PV/ET MF). Fifty-eight subjects had ≥1 non-driver mutation upon diagnosis. Mutations in mRNA splicing genes, especially in U2A...

Journal: :The Journal of clinical investigation 2014
Guangyao Kong Mark Wunderlich David Yang Erik A Ranheim Ken H Young Jinyong Wang Yuan-I Chang Juan Du Yangang Liu Sin Ruow Tey Xinmin Zhang Mark Juckett Ryan Mattison Alisa Damnernsawad Jingfang Zhang James C Mulloy Jing Zhang

Overactive RAS signaling is prevalent in juvenile myelomonocytic leukemia (JMML) and the myeloproliferative variant of chronic myelomonocytic leukemia (MP-CMML) in humans, and both are refractory to conventional chemotherapy. Conditional activation of a constitutively active oncogenic Nras (NrasG12D/G12D) in murine hematopoietic cells promotes an acute myeloproliferative neoplasm (MPN) that rec...

2016
Joseph A. Clara David A. Sallman Eric Padron

The myelodysplastic/myeloproliferative neoplasms (MDS/MPNs) are a unique group of hematologic malignancies characterized by concomitant myelodysplastic and myeloproliferative features. According to the 2008 WHO classification, the category includes atypical chronic myeloid leukemia (aCML), chronic myelomonocytic leukemia (CMML), juvenile myelomonocytic leukemia (JMML), MDS/MPN-unclassifiable (M...

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