Segmental neurofibromatosis type 5 (NF5) is a rare form of NF, in which the cutaneous and/or neural changes are confined to one region of the body. It is often underdiagnosed or undetected due to the absence of symptoms. Inheritance of NF is different from other types of NF. Intraosseous neurofibromas are rare tumors which develop from nerves supplying the periosteum or nerves following the int...

Intraosseous vascular lesions are rare conditions. They are most commonly seen in the vertebral column and skull; nevertheless, the mandible is a quite rare location. In this report, we present a case of intraosseous cavernous hemangioma in the mandible and discuss the clinical and radiological features. A 28-year-old male patient attended to our clinic with a complaint of painless swelling of ...

Intraosseous schwannoma is a rare benign neoplasm arising from Schwann cells of the nerve sheath and involving the substance of bone. Intraosseous schwannomas account for less than 0.2 % of primary bone tumors. The most common site of occurrence is the mandible, a characteristic traditionally attributed to the long intraosseous path of the inferior alveolar nerve. Here we report a case of intra...

BACKGROUND Lipoma in nasal region in a case of Pai syndrome is very rare. Very few cases of Pai syndrome with columellar lipoma with extension to septum and tip have been reported till date. CASE PRESENTATION We report a very rare form of nasal lipoma in a case of Pai syndrome with extension to septum and tip in a 4 year old female child. CONCLUSIONS Pai syndrome with columellar lipoma with...

BACKGROUND Mucoepidermoid carcinoma arises from major or minor salivary glands, making up 10% of salivary gland tumors. Intraosseous mucoepidermoid carcinomas are rare, and make up only 2% to 3% of all mucoepidermoid carcinomas. The t(11;19) and its CRTC1-MAML2 fusion gene transcript have been identified in mucoepidermoid carcinoma and are associated with a subset of mucoepidermoid carcinomas. ...

UNLABELLED Pleomorphic lipoma is a relatively uncommon entity, and is considered as a variant of spindle cell lipoma. Histologically, spindle cell lipoma/pleomorphic lipoma consists of varying quantity of mature fat, bland spindle cells and ropey collagen. In addition, pleomorphic lipoma is characterized by multinucleate giant cells, which possess the "floret-like" nuclei and marked pleomorphis...

BACKGROUND Hibernoma is a rare benign tumor of adults that is composed of multivacuolated adipocytes resembling brown fat cells. Hibernoma typically occurs in soft tissue, and intraosseous examples are very rare. Intraosseous hibernomas can radiologically mimic metastatic carcinoma and other tumorous conditions. METHODS To collect the intraosseous hibernomas, we searched the pathologic databa...

Infiltrating lipoma is a rare variety of lipoma, characterized by an infiltration of the adipose tissue of the muscles. Infiltrating lipomas are usually classified in two groups: intermuscular infiltrating lipoma and intramuscular infiltrating lipoma. Most are acquired, and they usually appear in middle-aged individuals. Exceptionally, they are congenital. In such cases they are not related to ...

intraosseous squamous cell carcinoma is a rare type of squamous cell carcinoma that requires accurate and early diagnose which is important due to its invasive feature. this article presents a rare case report on intraosseous carcinoma in a 33-year-old patient. the case was a 33-year-old man who was referred to oral disease department of babol college of dentistry complaining of chin pain. in t...

Lipoma of the cutaneous region is very common tumor. Most of cutaneous lipoma arises in the subcutaneous adipose tissue. When the tumor is composed exclusively mature lipocytes, the tumor is referred to as lipoma. When the tumor contains areas of capillary, it is called angiolipoma. When the tumor has rich fibrous tissue, it is called fibrolipoma. When the tumor consisted of spindle cells, it i...