نتایج جستجو برای: fibrillogenesis

تعداد نتایج: 604  

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2014
P Patrizia Mangione Riccardo Porcari Julian D Gillmore Piero Pucci Maria Monti Mattia Porcari Sofia Giorgetti Loredana Marchese Sara Raimondi Louise C Serpell Wenjie Chen Annalisa Relini Julien Marcoux Innes R Clatworthy Graham W Taylor Glenys A Tennent Carol V Robinson Philip N Hawkins Monica Stoppini Stephen P Wood Mark B Pepys Vittorio Bellotti

The Ser52Pro variant of transthyretin (TTR) produces aggressive, highly penetrant, autosomal-dominant systemic amyloidosis in persons heterozygous for the causative mutation. Together with a minor quantity of full-length wild-type and variant TTR, the main component of the ex vivo fibrils was the residue 49-127 fragment of the TTR variant, the portion of the TTR sequence that previously has bee...

2015
Wen-Jie Du Jing-Jing Guo Ming-Tao Gao Sheng-Quan Hu Xiao-Yan Dong Yi-Fan Han Fu-Feng Liu Shaoyi Jiang Yan Sun

Soluble amyloid β-protein (Aβ) oligomers, the main neurotoxic species, are predominantly formed from monomers through a fibril-catalyzed secondary nucleation. Herein, we virtually screened an in-house library of natural compounds and discovered brazilin as a dual functional compound in both Aβ42 fibrillogenesis inhibition and mature fibril remodeling, leading to significant reduction in Aβ42 cy...

2002
Paul Bornstein Vanessa Walsh Jennifer Tullis Emily Stainbrook John F. Bateman Sheriar G. Hormuzdi

The globular domain in the NH2-terminal propeptide (N-propeptide) of the pro 1(I) chain is largely encoded by exon 2 of the Col1a1 gene and has been implicated in a number of processes that are involved in the biogenesis, maturation, and function of type I collagen. These include intracellular chain association, transcellular transport and secretion, proteolytic processing of the precursor, fee...

Journal: :The Journal of Cell Biology 2002
Erik H.J. Danen Petra Sonneveld Cord Brakebusch Reinhard Fässler Arnoud Sonnenberg

We have studied the formation of different types of cell matrix adhesions in cells that bind to fibronectin via either alpha5beta1 or alphavbeta3. In both cases, cell adhesion to fibronectin leads to a rapid decrease in RhoA activity. However, alpha5beta1 but not alphavbeta3 supports high levels of RhoA activity at later stages of cell spreading, which are associated with a translocation of foc...

Journal: :The British journal of ophthalmology 1980
A J Dark B W Streeten

Greyish-white spots, varying in size, caused diagnostic problems in 2 patients with pre-invasive corneal carcinoma. Keratectomy specimens permitting light and electron microscopy indicated that the smaller spots predominating in one patient correlated with epithelial microcysts and vacuoles, while areas of parakeratosis accounted for the macroscopic white patches found in the other. A variety o...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید