نتایج جستجو برای: cmt1a

تعداد نتایج: 183  

Journal: :Journal of the Chinese Medical Association : JCMA 2006
Shun-Sheng Chen

Charcot-Marie-Tooth (CMT) disorders are an extremely heterogeneous group of diseases of the peripheral nervous system in humans, with a prevalence of around 1 in 2,500. To date, mutations in 30 genes have been reported in various CMT forms. In numerous CMT types, only the locus is known, but some CMT forms were shown not to be linked with any known locus. Genetic studies in CMT disorders cover ...

2017
Jing Li Bing Niu Xiaoling Wang Huaiqiang Hu Bingzhen Cao

RATIONALE Hereditary neuropathy with liability to pressure palsy (HNPP) is an episodic, multifocal neuropathy, with a typical clinical presentation of recurrent transient pressure palsies, which is induced by a PMP22 deletion. Another neuropathy caused by a PMP22 duplication is Charcot-Marie-Tooth disease type 1A (CMT1A). PMP22 is a gene coding a protein called peripheral myelin protein 22 (PMP...

Journal: :The Journal of neuroscience : the official journal of the Society for Neuroscience 2011
Burkhard Gess Dominik Röhr Robert Fledrich Michael W Sereda Ilka Kleffner Anne Humberg Johanna Nowitzki Jan-Kolja Strecker Hartmut Halfter Peter Young

Ascorbic acid (vitamin C) is necessary for myelination of Schwann cell/neuron cocultures and has shown beneficial effects in the treatment of a Charcot-Marie-Tooth neuropathy 1A (CMT1A) mouse model. Although clinical studies revealed that ascorbic acid treatment had no impact on CMT1A, it is assumed to have an important function in peripheral nerve myelination and possibly in remyelination. How...

Journal: :Brain : a journal of neurology 2004
Lionel Ginsberg Omar Malik Anthony R Kenton David Sharp John R Muddle Mary B Davis John B Winer Richard W Orrell Rosalind H M King

Classically, the course of Charcot-Marie-Tooth (CMT) disease is gradually progressive. We describe eight atypical patients who developed acute or subacute deterioration. Seven of these had genetically proven CMT disease type 1A (CMT1A) due to chromosome 17p11.2-12 duplication, and one had X-linked disease (CMTX) due to a mutation in the GJB1 gene. In this group there was sufficient clinical, el...

Journal: :Journal of medical genetics 2004
E Nelis J Berciano N Verpoorten K Coen I Dierick V Van Gerwen O Combarros P De Jonghe V Timmerman

C harcot-Marie-Tooth (CMT) disease is a clinically and genetically heterogeneous group of disorders that involve the peripheral nervous system. It is characterised by progressive distal neurogenic muscular atrophy and weakness that initially affects the peroneal muscles and later the hands. Charcot-Marie-Tooth disease type 1 (CMT1), also called hereditary motor and sensory neuropathy type I (HM...

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