نتایج جستجو برای: clinical exome sequencing

تعداد نتایج: 1271061  

Journal: :European Journal of Human Genetics 2011

2017
Sureni V Mullegama Phillip Jensik Chen Li Naghmeh Dorrani Sibel Kantarci Bruce Blumberg Wayne W Grody Samuel P Strom

Clinicians should consider that clinical exome sequencing provides the unique potential to disentangle complex phenotypes into multiple genetic etiologies. Further, functional studies on variants of uncertain significance are necessary to arrive at an accurate diagnosis for the patient.

2017
Maarten Otter Marijke Wevers Marline Pisters Rolph Pfundt Yvonne Vos Rutger Jan Nievelstein Constance Stumpel

Clinical geneticists, neurologists, psychiatrists, and other healthcare providers can learn from this case report that patients with a behavioral phenotype that includes a mild learning disability may also require a thorough examination, including brain MRI and whole-exome sequencing.

Whole Exome Sequencing (WES) has been increasingly utilized in genetic determinants of various inherited diseases. We identified a new variation in SERAC1 as the cause of 3-Methylglutaconic Aciduria (MEG), Deafness (D), Encephalopathy (E), and Leigh-like (L), MEGDEL syndrome using WES. We found an insertion, rs797045105 (chr6, 158571484, C>CCATG), in the SERAC1 gene with homozygous genotype in ...

2013
Daichi Shigemizu Akihiro Fujimoto Shintaro Akiyama Tetsuo Abe Kaoru Nakano Keith A. Boroevich Yujiro Yamamoto Mayuko Furuta Michiaki Kubo Hidewaki Nakagawa Tatsuhiko Tsunoda

The recent development of massively parallel sequencing technology has allowed the creation of comprehensive catalogs of genetic variation. However, due to the relatively high sequencing error rate for short read sequence data, sophisticated analysis methods are required to obtain high-quality variant calls. Here, we developed a probabilistic multinomial method for the detection of single nucle...

Journal: :The New England journal of medicine 2016
Maja Tarailo-Graovac Casper Shyr Colin J Ross Gabriella A Horvath Ramona Salvarinova Xin C Ye Lin-Hua Zhang Amit P Bhavsar Jessica J Y Lee Britt I Drögemöller Mena Abdelsayed Majid Alfadhel Linlea Armstrong Matthias R Baumgartner Patricie Burda Mary B Connolly Jessie Cameron Michelle Demos Tammie Dewan Janis Dionne A Mark Evans Jan M Friedman Ian Garber Suzanne Lewis Jiqiang Ling Rupasri Mandal Andre Mattman Margaret McKinnon Aspasia Michoulas Daniel Metzger Oluseye A Ogunbayo Bojana Rakic Jacob Rozmus Peter Ruben Bryan Sayson Saikat Santra Kirk R Schultz Kathryn Selby Paul Shekel Sandra Sirrs Cristina Skrypnyk Andrea Superti-Furga Stuart E Turvey Margot I Van Allen David Wishart Jiang Wu John Wu Dimitrios Zafeiriou Leo Kluijtmans Ron A Wevers Patrice Eydoux Anna M Lehman Hilary Vallance Sylvia Stockler-Ipsiroglu Graham Sinclair Wyeth W Wasserman Clara D van Karnebeek

BACKGROUND Whole-exome sequencing has transformed gene discovery and diagnosis in rare diseases. Translation into disease-modifying treatments is challenging, particularly for intellectual developmental disorder. However, the exception is inborn errors of metabolism, since many of these disorders are responsive to therapy that targets pathophysiological features at the molecular or cellular lev...

Journal: :Clinical genetics 2014
C Baquero-Montoya M C Gil-Rodríguez D Braunholz M E Teresa-Rodrigo C Obieglo B Gener T Schwarzmayr T M Strom P Gómez-Puertas B Puisac G Gillessen-Kaesbach A Musio F J Ramos F J Kaiser J Pié

To the Editor : Cornelia de Lange Syndrome (CdLS) is an autosomal dominant (NIPBL, SMC3 and RAD21 ) or Xlinked (SMC1A and HDAC8 ) congenital disorder, characterized by distinctive craniofacial appearance, growth retardation, intellectual disability and limb malformations (1). Currently, mutations in about 70% of the patients studied have been identified (1). However, recent studies have found l...

2017
Holly LaDuca Kelly D. Farwell Huy Vuong Hsiao-Mei Lu Wenbo Mu Layla Shahmirzadi Sha Tang Jefferey Chen Shruti Bhide Elizabeth C. Chao

BACKGROUND With the expanded availability of next generation sequencing (NGS)-based clinical genetic tests, clinicians seeking to test patients with Mendelian diseases must weigh the superior coverage of targeted gene panels with the greater number of genes included in whole exome sequencing (WES) when considering their first-tier testing approach. Here, we use an in silico analysis to predict ...

2014
Erwin Tantoso Lai-Ping Wong Bowen Li Woei-Yuh Saw Wenting Xu Peter Little Rick Twee-Hee Ong Yik-Ying Teo

Next-generation genotyping microarrays have been designed with insights from large-scale sequencing of exomes and whole genomes. The exome genotyping arrays promise to query the functional regions of the human genome at a fraction of the sequencing cost, thus allowing large number of samples to be genotyped. However, two pertinent questions exist: firstly, how representative is the content of t...

2015
Bart J.G. Broeckx Christophe Hitte Frank Coopman Geert E.C. Verhoeven Sarah De Keulenaer Ellen De Meester Thomas Derrien Jessica Alfoldi Kerstin Lindblad-Toh Tim Bosmans Ingrid Gielen Henri Van Bree Bernadette Van Ryssen Jimmy H. Saunders Filip Van Nieuwerburgh Dieter Deforce

By limiting sequencing to those sequences transcribed as mRNA, whole exome sequencing is a cost-efficient technique often used in disease-association studies. We developed two target enrichment designs based on the recently released annotation of the canine genome: the exome-plus design and the exome-CDS design. The exome-plus design combines the exons of the CanFam 3.1 Ensembl annotation, more...

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