نتایج جستجو برای: charcot marie

تعداد نتایج: 11416  

Journal: :Archives of Clinical and Medical Case Reports 2020

Journal: :Swiss Medical Forum ‒ Schweizerisches Medizin-Forum 2010

Journal: :Pediatric Neurology Briefs 2008

Journal: :JAMA neurology 2016
Kayla M D Cornett Manoj P Menezes Paula Bray Mark Halaki Rosemary R Shy Sabrina W Yum Timothy Estilow Isabella Moroni Maria Foscan Emanuela Pagliano Davide Pareyson Matilde Laurá Trupti Bhandari Francesco Muntoni Mary M Reilly Richard S Finkel Janet Sowden Katy J Eichinger David N Herrmann Michael E Shy Joshua Burns

IMPORTANCE Disease severity of childhood Charcot-Marie-Tooth disease (CMT) has not been extensively characterized, either within or between types of CMT to date. OBJECTIVE To assess the variability of disease severity in a large cohort of children and adolescents with CMT. DESIGN, SETTING, AND PARTICIPANTS A cross-sectional study was conducted among 520 children and adolescents aged 3 to 20...

Journal: :Frontiers in ophthalmology 2021

Oculomotor palsy with cyclic spasms is an extremely rare condition whose exact pathophysiology remains a mystery. We followed boy from the onset of symptoms at age ten months until 15 years and documented case video oculography. In addition, he was diagnosed hereditary motor sensory neuropathy (Charcot-Marie-Tooth disease type 1). Although pure coincidence cannot be ruled out, it conceivable th...

2013
Madhumala K Sadanandappa Mani Ramaswami

A Drosophila model for a neurological disorder called type 2B Charcot-Marie-Tooth disease reveals that it has its origins in a partial loss of function, rather than a gain of function, which points to the need for a new therapeutic approach.

2016
Marta Romani Cybel Mehawej Tommaso Mazza Andre Mégarbané Enza Maria Valente

Charcot-Marie-Tooth neuropathy type 4 (CMT4) comprises a large group of genetically heterogeneous progressive sensory motor neuropathies characterized by autosomal recessive inheritance. Among these, CMT4B includes 3 forms related to genes of the myotubularin family, namely CMT4B1 (MTMR2), CMT4B2 (MTMR13/SBF2), and CMT4B3 (MTMR5/SBF1).

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