INTRODUCTION The clinical behavior of desmoid tumors can be unpredictable, particularly when they arise in the ante-partum or post-partum period. We present a case of an intra-abdominal desmoid tumor that was identified in the ante-partum period, progressed rapidly in the post-partum period, and was subsequently resected. PRESENTATION OF CASE The patient is a 19 year-old female who was found ...

Desmoid tumors are rare soft tissue tumors considered to have locally infiltrative features without distant metastasis until now. Although they are most commonly intraabdominal, very few cases have extra-abdominal locations. The origin of intrathoracic desmoid tumors is predominantly the chest wall with occasional involvement of pleura. True intrathoracic primary desmoid tumors with no involvem...

The local control of desmoid tumors constitutes a continuing treatment dilemma due to its high recurrence rates. The purpose of this systematic review was to critically examine the current treatment of these rare tumors and to specifically evaluate the local failure and response rates of surgery, radiation and systemic therapy. We comprehensively searched the literature for relevant studies acr...

OBJECTIVE To construct a postoperative nomogram to estimate the risk of local recurrence for patients with desmoid tumors. BACKGROUND The standard management of desmoid tumors is resection, but many recur locally. Other options include observation or novel chemotherapeutics, but little guidance exists on selecting treatment. METHODS Patients undergoing resection during 1982-2011 for primary...

BACKGROUND Desmoid tumor is a rare entity, and most desmoid tumors are located in abdominal wall or extra-abdominal tissues. Occurrence of desmoid tumor in mesentry is extremely rare. CASE PRESENTATION we report a mesenteric desmoid tumor in a 73-years-old woman who had undergone total gastrectomy reconstructed with jejunal pouch interposition for gastric carcinoma. After 1 year, a tumor was ...

BACKGROUND Aggressive fibromatosis is a rare but invasive tumor infiltrating widely between fascia and muscle fibers. It has a high tendency to be locally recurrent despite complete resection. Effectiveness of adjuvant treatment for aggressive fibromatosis including radiotherapy, pharmacological agents, hormonal treatments, and chemotherapy have been previously reported. The purpose of this art...

Abstract Background The term fibromatosis refers to a spectrum of soft tissue tumors resulting from the unbridled proliferation fibroblasts, with high infiltrative power. It is rare neoplasm, an incidence about 3 cases per million. Most common sites include abdominal wall and cavity, chest wall, scapular area, limbs, rarely affecting axilla. Imaging plays major role in surgical planning clinica...

La fibromatosis ligamentoide (fibromatosis invasiva, fibroma desmoide) es una neoplasia mesenquimatosa, intermedia entre los tumores benignos y malignos, de origen fibroso, que manera infrecuente puede afectar el mesenterio. Se presenta caso un paciente masculino con tumoración fibrosa intraabdominal a nivel raíz realiza revisión la literatura.

Desmoids are rare, benign fibromatous lesions, which can arise in patients with familial adenomatous polyposis (FAP), a disorder caused by germline adenomatous polyposis coli (APC) gene mutation. This study investigated the risk of desmoids in FAP, the relation between specific APC gene mutations and desmoid formation, and the clinical characteristics ofFAP patients with desmoids. Eighty three ...

Introduction: Desmoid fibromatosis is an extremely rare but locally aggressive soft tissue tumor. When radical resection is indicated, the surgical team faces the challenge of abdominal wall reconstruction, for which optimal technique is still debated. We present the case of a giant abdominal wall desmoid tumor identified in the ante-partum period, showing a growth in the post-partum period whi...