total anomalous pulmonary venous connection (tapvc) is an anomaly in which the pulmonary veins are directly connected to one of the systemic veins or drain into the right atrium. management of pulmonary hypertension after the total correction of this congenital cardiac anomaly is very important. unligation of the vertical vein in the supracardiac type of this anomaly can be a draining pathway f...

A child with the isolated anomaly of azygos continuation of the inferior vena cava is presented. The interest of this abnormality lies in its detection as a mediastinal mass on the chest radiograph. Computed tomography with intravenous contrast enhancement is the method of choice to diagnose this venous anomaly. Awareness of the caval-azygos abnormality is important to surgeons and cardiologist...

A supernumerary kidney is a rare congenital anomaly of the urinary tract. Association of supernumerary kidney with horseshoe kidney is even rarer and true incidence of this anomaly is not known because of its infrequent occurrence. Because of the wide range of associated anomalies and the rarity of such cases, diagnosis and management remains difficult. Ultrasound, Intra venous urography/ Compu...

KILT syndrome is a rare condition composing the triad of kidney and inferior vena cava anomaly and extensive venous thrombosis. We present a case of newly diagnosed KILT syndrome in a 41-years-old gentleman presenting with loin pain and fever. Reviewing previous case reports, KILT syndrome is usually an incidental finding on imaging studies and there is a wide scope of initial clinical presenta...

Klippel Trenaunay syndrome refers to a rare congenital anomaly which is characterized by capillary malformation, venous malformation and sometimes lymphatic malformation associated with overgrowth of a limb, with soft tissue hypertrophy and/or bony hypertrophy. The anomaly, if present, is present at birth and usually involves the lower limbs as well as portion of trunk, face, uppper limb or hea...

Vascular anomalies are a heterogeneous group of congenital blood vessel disorders more typically referred to as birthmarks. Subcategorized into vascular tumors and malformations, each anomaly is characterized by specific morphology, pathophysiology, clinical behavior, and management approach. Hemangiomas are the most common vascular tumors. Lymphatic, capillary, venous, and arteriovenous malfor...