introduction: notochord. although histologically benign, these tumors are locally aggressiveand present significant managment challenges . there arew some studies onevaluated the location, age and gender of the patients with chordoma in tworeferral centers in tehran.chordoma cases but there was no study about iranian cases. in this study weskull base chordomas are rare neoplasms arising from th...

We report a child with osteopetrosis, oxycephaly and Chiari type I malformation who presented with raised intracranial pressure. During cranial expansion surgery the patient developed sudden cardiac arrest which we believe was probably related to the Chiari malformation. The case highlights a previously unrecognized association between osteopetrosis, craniosynostosis and a persistently open fon...

gastrointestinal (gi) bleeding in pediatric patients has several causes. vascular malformation of the small bowel is a rare disease leading to pediatric gi bleeding. to our knowledge, few reports describe ultrasound and computed tomography findings of venous malformations involving the small bowel. we present a case of long-segmental and circumferential vascular malformation that led to gi blee...

Currarino syndrome is a rare congenital malformation characterised by the triad of: an anorectal malformation, sacral bony defect and presacral mass. One but possible anal canal duplication, anomaly which not only most distal also rarest form of digestive tract duplication. We present case four-year-old female who had complete including

A 23-year-old male motorcyclist experienced blunt head trauma with loss of consciousness, headache and vomiting, epistaxis right otorrhagia after a collision motor vehicle. Fractures involving the parietal temporal bones, as well acute subdural subarachnoid hemorrhage were identified on cranial facial CT scan. On independent evaluation imaging study, subtle but distinct fracture line in skull b...

the clivus is the surface of a portion of the occipital and sphenoid bones in the base of the skull. (1)it is surrounded by the neurovascular structures of the brainstem, as well as internal carotid arteries. tumors of the clivus can be benign (chordoma)or malignant (chondrosarcoma).(2) chordomas are rare, aggressive, slow-growing, invasive, and locally destructive tumors that arise from the no...

ollier’s syndrome, a variant of multiple enchondromatosis, is a rare disease with an estimated prevalence of 1/100,000, characterized by multiple enchondromas, asymmetrically involving small bones of the hands and feet, especially the proximal phalanges. intracranial enchondromas, such as those arising from the skull base are extremely rare. herein, we report a 25-year-old female, known case of...