نتایج جستجو برای: f8 protein

تعداد نتایج: 1235400  

Journal: :Blood 2013
Corien L Eckhardt Alice S van Velzen Marjolein Peters Jan Astermark Paul P Brons Giancarlo Castaman Marjon H Cnossen Natasja Dors Carmen Escuriola-Ettingshausen Karly Hamulyak Daniel P Hart Charles R M Hay Saturnino Haya Waander L van Heerde Cedric Hermans Margareta Holmström Victor Jimenez-Yuste Russell D Keenan Robert Klamroth Britta A P Laros-van Gorkom Frank W G Leebeek Ri Liesner Anne Mäkipernaa Christoph Male Evelien Mauser-Bunschoten Maria G Mazzucconi Simon McRae Karina Meijer Michael Mitchell Massimo Morfini Marten Nijziel Johannes Oldenburg Kathelijne Peerlinck Pia Petrini Helena Platokouki Sylvia E Reitter-Pfoertner Elena Santagostino Piercarla Schinco Frans J Smiers Berthold Siegmund Annarita Tagliaferri Thynn T Yee Pieter Willem Kamphuisen Johanna G van der Bom Karin Fijnvandraat

Neutralizing antibodies (inhibitors) toward factor VIII form a severe complication in nonsevere hemophilia A, profoundly aggravating the bleeding pattern. Identification of high-risk patients is hampered by lack of data that take exposure days to therapeutic factor VIII concentrates into account. In the INSIGHT study, we analyzed the association between F8 mutation and inhibitor development in ...

2012
Yuji Kashiwakura Jun Mimuro Akira Onishi Masaki Iwamoto Seiji Madoiwa Daiichiro Fuchimoto Shunichi Suzuki Misae Suzuki Shoichiro Sembon Akira Ishiwata Atsushi Yasumoto Asuka Sakata Tsukasa Ohmori Michiko Hashimoto Satoko Yazaki Yoichi Sakata

Hemophilia A is a common X chromosome-linked genetic bleeding disorder caused by abnormalities in the coagulation factor VIII gene (F8). Hemophilia A patients suffer from a bleeding diathesis, such as life-threatening bleeding in the brain and harmful bleeding in joints and muscles. Because it could potentially be cured by gene therapy, subhuman animal models have been sought. Current mouse hem...

2011
Sonja Kriks Jae-Won Shim Jinghua Piao Yosif M. Ganat Dustin R. Wakeman Zhong Xie Luis Carrillo-Reid Viviane Tabar Lorenz Studer

Human pluripotent stem cells (PSCs) are a promising source of cells for applications in regenerativemedicine.Directed differentiation of PSCs into specialized cells such as spinal motoneurons or midbrain dopamine (DA) neurons has been achieved. However, the effective use of PSCs for cell therapy has lagged behind.Whereasmouse PSCderived DA neurons have shown efficacy in models of Parkinson’s di...

پایان نامه :وزارت علوم، تحقیقات و فناوری - دانشگاه تربیت مدرس - دانشکده کشاورزی 1391

aflp یک ابزار قدرتمند برای تشخیص رونوشت هایی با فراوانی کم است و می تواند بعنوان یک روش کارآمد برای جداسازی ژنهایی که بطور متمایز بیان می شوند، بکار رود. بنابراین القا متمایز ژنها در گندم ( رقم چمران و مرودشت) در پاسخ به قارچ m.graminicola بوسیله آنالیز cdna-aflp مورد مطالعه قرار گرفت . در ابتدا گیاهان بوسیله بیمارگر مایه زنی شدند. نمونه برداری در 6 نقطه زمانی(0، 12، 24، 48، 72 و 96 ساعت) بعد ا...

Journal: :The Journal of biological chemistry 2000
S R Yeh M Couture Y Ouellet M Guertin D L Rousseau

The homodimeric hemoglobin (HbN) from Mycobacterium tuberculosis displays an extremely high oxygen binding affinity and cooperativity. Sequence alignment with other hemoglobins suggests that the proximal F8 ligand is histidine, the distal E7 residue is leucine, and the B10 position is occupied by tyrosine. To determine how these heme pocket residues regulate the ligand binding affinities and ph...

Journal: :Blood 2013
Samantha C Gouw H Marijke van den Berg Kathelijn Fischer Günter Auerswald Manuel Carcao Elizabeth Chalmers Hervé Chambost Karin Kurnik Ri Liesner Pia Petrini Helen Platokouki Carmen Altisent Johannes Oldenburg Beatrice Nolan Rosario Pérez Garrido M Elisa Mancuso Anne Rafowicz Mike Williams Niels Clausen Rutger A Middelburg Rolf Ljung Johanna G van der Bom

The objective of this study was to examine the association of the intensity of treatment, ranging from high-dose intensive factor VIII (FVIII) treatment to prophylactic treatment, with the inhibitor incidence among previously untreated patients with severe hemophilia A. This cohort study aimed to include consecutive patients with a FVIII activity < 0.01 IU/mL, born between 2000 and 2010, and ob...

2016
Ming Chen Shun-Ping Chang Gwo-Chin Ma Wen-Hsian Lin Hsin-Fu Chen Shee-Uan Chen Horng-Der Tsai Feng-Po Tsai Ming-Ching Shen

Preimplantation genetic diagnosis (PGD) is a powerful tool to tackle the transmission of monogenic inherited disorders in families carrying the diseases from generation to generation. It currently remains a challenging task, despite PGD having been developed over 25 years ago. The major difficulty is it does not have an easy and general formula for all mutations. Different gene locus needs indi...

Journal: :Protein engineering, design & selection : PEDS 2010
Roberto Sommavilla Nadine Pasche Eveline Trachsel Leonardo Giovannoni Christoph Roesli Alessandra Villa Dario Neri Manuela Kaspar

Proinflammatory cytokines have been used for several years in patients with advanced cancer but their administration is typically associated with severe toxicity hampering their application to therapeutically active regimens. This problem can be overcome by using immunocytokines (cytokines fused to antibody or antibody fragments) which selectively deliver the active cytokine to the tumor enviro...

2017
Szu-Ping Huang Tzu-Ming Ho Chih-Wen Yang Ya-Ju Chang Jie-Fu Chen Ning-Sing Shaw Jia-Cherng Horng Shih-Lan Hsu Ming-Yuan Liao Li-Chen Wu Ja-an Annie Ho

Luobuma (Apocynum venetum L. (AVL)) is a popular beverage in Asia and has been reportedly to be associated with the bioactivities such as cardiotonic, diuretic, antioxidative, and antihypertensive. However, its biofunction as chemoprevention activity is seldom addressed. Herein, we aimed to characterize the anti-androgen-insensitive-prostate-cancer (anti-AIPC) bioactive compounds of Luobuma, an...

Journal: :Blood 2015
Devi Gunasekera Ruth A Ettinger Shelley Nakaya Fletcher Eddie A James Maochang Liu John C Barrett Janice Withycombe Dana C Matthews Melinda S Epstein Richard J Hughes Kathleen P Pratt

African American hemophilia A (HA) patients experience a higher incidence of neutralizing anti-factor VIII (FVIII) antibodies ("inhibitors") vis-à-vis white patients. Nonsynonymous single-nucleotide polymorphisms (ns-SNPs) in the F8 gene encoding FVIII-H484, FVIII-E1241, and FVIII-V2238 are more prevalent in African Americans. This study tested the hypothesis that immune responses to these site...

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