Congenital hearing loss is relatively frequent and has serious negative consequences if it is not diagnosed and treated during the first few months of life. Babies with hearing loss who are identified early and provided with appropriate intervention develop better language, cognitive, and social skills. As a result of improvements in screening equipment and procedures, newborn hearing screening...

Malformations of bony inner ear are rare anomalies occurring in approximately 20% of patients with congenital sensorineural hearing loss. Conductive hearing loss is usually associated with abnormalities of the external and middle ear. Recent reports of patients with lateral semicircular canal malformations indicate inner ear malformations to be associated with sensorineural or conductive hearin...

OBJECTIVES/HYPOTHESIS Compare the epidemiology of pediatric unilateral sensorineural hearing loss before and after implementation of universal newborn hearing screening in Missouri. STUDY DESIGN Inception cohort. METHODS Charts of 134 children born between January 1, 1990 and December 31, 2007, diagnosed with unilateral sensorineural hearing loss at a single institution in Missouri were rev...

background: taxi drivers have the most important role in the public transport services. they are exposed to various harmful agents and occupational hazards. noise is a harmful occupational factors and hearing loss is its most important effect. protection of drivers against hearing loss is essential. this study was performed to determine the prevalence of hearing loss among taxi and agency drive...

Studies of congenital and early-onset deafness have demonstrated that an absence of peripheral sound-evoked activity in the auditory nerve causes pathological changes in central auditory structures. The aim of this study was to establish whether progressive acquired hearing loss could lead to similar brain changes that would degrade the precision of signal transmission. We used complementary ph...

In this review the authors discuss the physiopathologic and electrophysiologic changes of the inner ear in Meniere's disease, otosclerosis, ototoxicity, acoustic neuroma, presbycusis, noise-induced hearing loss, metabolic hearing loss, perilymphatic fistula, syphilis, autoimmune inner ear disease, congenital genetic hearing loss, and viral labyrinthitis. The etiology and pathogenesis of hearing...

OBJECTIVE To study a family with inner ear malformations and sensorineural hearing loss. DESIGN Clinical, radiological, and genetic study of the members of a family with different degrees of sensorineural hearing loss. RESULTS The males in the family manifested profound congenital hearing loss with severe inner ear malformations, while the only affected female had progressive hearing loss t...

Early hearing detection and intervention programs have become the standard of care to ensure optimal outcomes for infants with hearing loss, their families and society at large. The overwhelming majority of infants with congenital or early-onset permanent bilateral hearing loss are however born in developing countries like South Africa where services are scarce and awareness poor. Despite its c...

OBJECTIVES To compare the prevalence of congenital cytomegalovirus (CMV) infection in Washington State in children with hearing loss (HL) and the general population and to compare the characteristics of HL in children with and without congenital CMV infection. DESIGN Matched case-control; case cohort. SETTING Regional pediatric hospital, Washington State Department of Health (WSDOH). PATI...

Hearing acuity was assessed in 45 children with sporadic congenital hypothyroidism during adequate long-term treatment. Otoscopy was performed in each and additional tympanometry in some of them. Secretory otitis media was found in 6 and was treated medically or by inserting grommets in the eardrum. In these children, hearing acuity was assessed after the otitis had been cured. Hearing acuity w...