OBJECTIVE To evaluate general health condition of children operated for esophageal atresia, including complications from gastrointestinal tract and skeletal defects. METHODS Between 1990 and 2005, 77 patients were operated for esophageal atresia in the Polish Mothers Health Memorial Hospital. The study was based on retrospective analysis of medical case records of all children with esophageal...

Pulmonary atresia with intact ventricular septum is the complete obstruction of the right ventricular outflow tract due to pulmonary valve atresia in the absence of ventricular septal defect. Pulmonary flow is dependent on the ductus arteriosus. Other morphological anomalies are also present. Aortic stenosis in association with pulmonary atresia with intact ventricular septum is extremely infre...

Hepatobiliary ultrasound is the most common initial diagnostic modality in early detection of biliary atresia. It not gold standard, but hepatobiliary examination can be used to determine appropriate further management. Objective: To determined value as a predictor atresia cholestasis infants. Methods: This was an observational study with test validity cholangiography standard. The research sub...

OBJECTIVE To present epidemiologic data on the relatively rare malformation choanal atresia, based on a large collection of material and with special stress on the significance of the so-called CHARGE (coloboma, heart defect, choanal atresia, retarded growth and development, genital anomaly, and ear defect with deafness) association. METHODS Data from three large registries of congenital malf...

Congenital esophageal atresia needs to be surgically corrected as soon as possible. Some will present with post surgical stricture that needs to be dilated by a balloon dilator. This procedure is difficult in premature born due to infant esophageal size and availability of equipments. We herby report the first case in a premature infant with post surgical esophageal stricture of esophageal atre...

BACKGROUND Small gut atresia is a common neonatal surgical problem. Early diagnosis and timely management of the neonate can reduce mortality and morbidity in these patients. The aim of this study was to note the causes of mortality and morbidity in these neonates. METHODS This was a prospective study conducted at Lady Reading Hospital (LRH) Peshawar from August 2007 to August 2009. All patie...

Atresia of the colon is a rare anomaly with an incidence of between 1:20,000 and 1:66,000 live births being reported. Hirschsprung's disease association with Colonic atresia is usually diagnosed after several failures of intestinal anastomoses. We herein report one of the first patients in the literature diagnosed before a therapeutic challenge. A 2-day-old female was admitted with severe abdom...

Forty cases of left atrioventricular valve (LAV) atresia without aortic stenosis or atresia were reviewed. Thirty-one had mitral atresia and nine had left tricuspid atresia. Eleven had associated pulmonary outflow tract obstruction. Twenty-two (55%) underwent cardiac catheterization and 12 had more than one study. Left atrial pressure was normal in seven infants younger than 2 weeks of age. Twe...

PURPOSE Anorectal malformations are often associated with other anomalies, reporting frequency with 40-70%. Gastrointestinal anomalies have been known to be relatively less common than associated anomalies of other organ system. This study was performed to assess a distinctive feature of cases associated with esophageal atresia. METHODS Clinical data (from January 2000 through December 2011) ...

Atresia of the distal ileum concurrent with ileocaecal valve agenesis is one of the rare types of intestinal atresia with very few reports in the literature. We herein present a case of type II distal ileal atresia, ileocaecal valve agenesis and volvulus of the ileum and the terminal jejunum with a history of depression, anorexia and failure to pass meconium. On necropsy, volvulus of the ileum ...