نتایج جستجو برای: anophthalmia

تعداد نتایج: 586  

2017
Tanya Bardakjian Max Krall Di Wu Richard Lao Paul Ling-Fung Tang Eunice Wan Sarina Kopinsky Adele Schneider Pui-yan Kwok Anne Slavotinek

Purpose The genetic causes of anophthalmia, microphthalmia and coloboma remain poorly understood. Missense mutations in Growth/Differentiation Factor 3 (GDF3) gene have previously been reported in patients with microphthalmia, iridial and retinal colobomas, Klippel-Feil anomaly with vertebral fusion, scoliosis, rudimentary 12th ribs and an anomalous right temporal bone. We used whole exome sequ...

Journal: :American journal of human genetics 2005
Nicola K Ragge Alison G Brown Charlotte M Poloschek Birgit Lorenz R Alex Henderson Michael P Clarke Isabelle Russell-Eggitt Alistair Fielder Dianne Gerrelli Juan Pedro Martinez-Barbera Piers Ruddle Jane Hurst J Richard O Collin Alison Salt Simon T Cooper Pamela J Thompson Sanjay M Sisodiya Kathleen A Williamson David R Fitzpatrick Veronica van Heyningen Isabel M Hanson

Major malformations of the human eye, including microphthalmia and anophthalmia, are examples of phenotypes that recur in families yet often show no clear Mendelian inheritance pattern. Defining loci by mapping is therefore rarely feasible. Using a candidate-gene approach, we have identified heterozygous coding-region changes in the homeobox gene OTX2 in eight families with ocular malformations...

2013
Christina Gerth-Kahlert Kathleen Williamson Morad Ansari Jacqueline K Rainger Volker Hingst Theodor Zimmermann Stefani Tech Rudolf F Guthoff Veronica van Heyningen David R FitzPatrick

Clinical evaluation and mutation analysis was performed in 51 consecutive probands with severe eye malformations - anophthalmia and/or severe microphthalmia - seen in a single specialist ophthalmology center. The mutation analysis consisted of bidirectional sequencing of the coding regions of SOX2, OTX2, PAX6 (paired domain), STRA6, BMP4, SMOC1, FOXE3, and RAX, and genome-wide array-based copy ...

Journal: :Birth Defects Research Part C: Embryo Today: Reviews 2015

Journal: :Genetics 1954
L G Browman

ICROPHTHALMIA has been reported in a number of rat colonies M (JONES 1925; KING 1931; HAIN 1936; BROWMAN 1941, 1943; QUISSENBERRY and BROWN 1942 ; CAMPBELL 1944). Published reports indicate that not only the embryological development but also the final eye condition may be quite varied in the several colonies (see BROWMAN and RAMSEY 1943 and CAMPBELL 1944). The mode of inheritance of this chara...

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