Dent’s disease (MIM #300009) is a rare X-linked disorder characterized by various degrees of proximal tubular (PT) dysfunction, nephrocalcinosis and nephrolithiasis. The exact prevalence is unknown. The disease was first reported by Dent and Friedman, who described two males with vitamin D resistant rickets, hypercalciuria and low molecular weight proteinuria (LMWP) (Dent & Friedman, 1964). Bas...

1. Closed ideals. (1.1) Definition. Let 5 be an arbitrary set, and 2 a Boolean ring of subsets of 5. The algebra B(S, 2) consists of all uniform limits of finite linear combinations of characteristic functions of sets in 2. The norm in B(S, 2) is given by the formula ||/|| =SupseS \f(s) | • This definition is slightly more general than that given in [l ] where 2 is required to be a field of set...

This article introduces various Boolean operators which are used in discussing the properties and stability of a 2's complement circuit. We present the deenitions and related theorems for the following logical operators which include negative input/output: 'and2a', 'or2a', 'xor2a' and 'nand2a', 'nor2a', etc. We formalize the concept of a 2's complement circuit, deene the structures of comple-me...

The structure of a 2-deoxystreptamine (DOS) precursor named S-11-P, which was isolated by using a DOS negative mutant derived from a xylostasin-producing strain of Bacillus circulans B15M, has been elucidated as (1 L)-1,3,5/2,4,-5-aminocyclohexanetetrol by comparison with an authentic specimen, which was synthesized from kanamycin A.