نتایج جستجو برای: ژن kcnj11

تعداد نتایج: 16247  

Journal: :Diabetes 2006
Kenju Shimomura Christophe A J Girard Peter Proks Joanna Nazim Jonathan D Lippiat Franco Cerutti Renata Lorini Sian Ellard Andrew T Hattersley Fabrizio Barbetti Frances M Ashcroft

Heterozygous mutations in the human Kir6.2 gene (KCNJ11), the pore-forming subunit of the ATP-sensitive K(+) channel (K(ATP) channel), are a common cause of neonatal diabetes. We identified a novel KCNJ11 mutation, R50Q, that causes permanent neonatal diabetes (PNDM) without neurological problems. We investigated the functional effects this mutation and another at the same residue (R50P) that l...

2017
E. De Franco R. Caswell J. A. L. Houghton V. Iotova A. T. Hattersley S. Ellard

AIMS An early genetic diagnosis of neonatal diabetes guides clinical management and results in improved treatment in ~ 40% of patients. In the offspring of individuals with neonatal diabetes, a prenatal diagnosis allows accurate estimation of the risk of developing diabetes and, eventually, the most appropriate treatment for the baby. In this study, we performed non-invasive prenatal genetic te...

2013
Matthijs L. Becker Ewan R. Pearson Ivan Tkáč

Oral antidiabetic drugs (OADs) are used for more than a half-century in the treatment of type 2 diabetes. Only in the last five years, intensive research has been conducted in the pharmacogenetics of these drugs based mainly on the retrospective register studies, but only a handful of associations detected in these studies were replicated. The gene variants in CYP2C9, ABCC8/KCNJ11, and TCF7L2 w...

2013
Maria Carla Proverbio Eleonora Mangano Alessandra Gessi Roberta Bordoni Roberta Spinelli Rosanna Asselta Paola Sogno Valin Stefania Di Candia Ilaria Zamproni Cecilia Diceglie Stefano Mora Manuela Caruso-Nicoletti Alessandro Salvatoni Gianluca De Bellis Cristina Battaglia

Congenital hyperinsulinism of infancy (CHI) is a rare disorder characterized by severe hypoglycemia due to inappropriate insulin secretion. The genetic causes of CHI have been found in genes regulating insulin secretion from pancreatic β-cells; recessive inactivating mutations in the ABCC8 and KCNJ11 genes represent the most common events. Despite the advances in understanding the molecular pat...

2014
Aliya Jiwani David Himmelstein Steffie Woolhandler James G Kahn

BACKGROUND The United States' multiple-payer health care system requires substantial effort and costs for administration, with billing and insurance-related (BIR) activities comprising a large but incompletely characterized proportion. A number of studies have quantified BIR costs for specific health care sectors, using micro-costing techniques. However, variation in the types of payers, provid...

2012
Christiane Winkler Jennifer Raab Harald Grallert Anette-Gabriele Ziegler

AIM To investigate whether type 2 diabetes susceptibility genes and body weight influence the development of islet autoantibodies and the rate of progression to type 1 diabetes. METHODS Genotyping for single nucleotide polymorphisms (SNP) of the type 2 diabetes susceptibility genes CDKAL1, CDKN2A/2B, FTO, HHEX-IDE, HMGA2, IGF2BP2, KCNJ11, KCNQ1, MTNR1B, PPARG, SLC30A8 and TCF7L2 was obtained ...

Journal: :The New England journal of medicine 2004
Anna L Gloyn Ewan R Pearson Jennifer F Antcliff Peter Proks G Jan Bruining Annabelle S Slingerland Neville Howard Shubha Srinivasan José M C L Silva Janne Molnes Emma L Edghill Timothy M Frayling I Karen Temple Deborah Mackay Julian P H Shield Zdenek Sumnik Adrian van Rhijn Jerry K H Wales Penelope Clark Shaun Gorman Javier Aisenberg Sian Ellard Pål R Njølstad Frances M Ashcroft Andrew T Hattersley

BACKGROUND Patients with permanent neonatal diabetes usually present within the first three months of life and require insulin treatment. In most, the cause is unknown. Because ATP-sensitive potassium (K(ATP)) channels mediate glucose-stimulated insulin secretion from the pancreatic beta cells, we hypothesized that activating mutations in the gene encoding the Kir6.2 subunit of this channel (KC...

Journal: :The Journal of clinical investigation 2008
Sara E Pinney Courtney MacMullen Susan Becker Yu-Wen Lin Cheryl Hanna Paul Thornton Arupa Ganguly Show-Ling Shyng Charles A Stanley

Congenital hyperinsulinism is a condition of dysregulated insulin secretion often caused by inactivating mutations of the ATP-sensitive K+ (KATP) channel in the pancreatic beta cell. Though most disease-causing mutations of the 2 genes encoding KATP subunits, ABCC8 (SUR1) and KCNJ11 (Kir6.2), are recessively inherited, some cases of dominantly inherited inactivating mutations have been reported...

Journal: :Diabetes 2009
Yasuharu Tabara Haruhiko Osawa Ryuichi Kawamoto Hiroshi Onuma Ikki Shimizu Tetsuro Miki Katsuhiko Kohara Hideichi Makino

OBJECTIVE The present study was conducted to confirm possible associations between candidate genes from genome-wide association studies and type 2 diabetes in Japanese diabetic patients and a community-based general population. A total of 11 previously reported single-nucleotide polymorphisms (SNPs) from the TCF7L2, CDKAL1, HHEX, IGF2BP2, CDKN2A/B, SLC30A8, and KCNJ11 genes were analyzed. RES...

2003
Anna L. Gloyn Michael N. Weedon Katharine R. Owen Martina J. Turner Bridget A. Knight Graham Hitman Mark Walker Jonathan C. Levy Mike Sampson Stephanie Halford Mark I. McCarthy Andrew T. Hattersley Timothy M. Frayling

The genes ABCC8 and KCNJ11, which encode the subunits sulfonylurea receptor 1 (SUR1) and inwardly rectifying potassium channel (Kir6.2) of the -cell ATPsensitive potassium (KATP) channel, control insulin secretion. Common polymorphisms in these genes (ABCC8 exon 16–3t/c, exon 18 T/C, KCNJ11 E23K) have been variably associated with type 2 diabetes, but no large ( 2,000 subjects) case-control stu...

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