To study the sandstorm resistance design of civil structures and transportation infrastructures, flow fields with various grain concentrations were simulated by windblown sand tunnel. The results show that concentration profile presents an exponential decay form before critical wind speed; as test speed increases, decreases initially increases afterwards height, characteristic height moving whi...

The Schwartz-Jampel Syndrome (SJS) is a very rare condition characterised by Constant fìndings such as typical facial appearance, muscle hypertrophy and continuous muscle activity. Other fìndings are more or less frequently associated, especially skeletai abnormalities, including dwarfism or anyway short stature. The Authors review thè literature about this condition analysing thè clinical pict...

Joong Geun Lee, Sang Hyub Lee, Seung Hyun Jeon, Jin Il Kim, Koo Han Yoo From the Department of Urology, School of Medicine, Kyung Hee University, Seoul, Korea Silver-Russel syndrome (SRS) is a disorder present at birth that involves poor growth, low birth weight, differences in the size of the two sides of the body, and genital anomalies. The diagnosis is based on distinct prenatal growth restr...

Background Turner syndrome (TS) occurs in one 2000-2500 live female births and is associated with short stature, premature ovarian failure, and a range of other phenotypic features. Girls with TS achieve an average adult height 20cm shorter than their mid-parenteral height if they didn’t receive treatment. Growth hormone (GH) treatment was associated with highly significant gains in growth and ...

Turner syndrome (TS), is the most common chromosomal abnormality in females. TS is caused by haploinsufficiency of the short arm of X-chromosome, and is usually diagnosed by karyotyping which is time-consuming, expensive and unfeasible for population screening. Neonatal diagnosis of TS permits detection of associated malformations, appropriate therapy for short stature and puberty, thus improvi...

Nijmegen breakage syndrome (NBS), a rare autosomal recessive condition also known as ataxia telangiectasia (AT) variants VI and V2, is characterised by microcephaly, typical facies, short stature, immunodeficiency, and chromosomal instability. We report the clinical, immunological, chromosomal, and cell biological findings in 42 patients who are included in the NBS Registry in Nijmegen. The imm...

Smoke layer interface height is an important parameter in fire safety science. In this paper, two methods are proposed on the basis of integral ratio method and least squares method. a series experiments were conducted 1:10 scale model tunnel for determining smoke fire. The determined by new have been compared with other existing approaches, including method, N-percentage rule. comparison resul...

Air is transported downstream by the water flow in a free-flow spillway tunnel, resulting high negative pressure, which causes gate vibration and cavitation. In this research work, physical model of tunnel was used to investigate effects surface velocity area residual cross sections on air movements. The results demonstrate that distribution forms an S-shaped curve. As increases or decreases, i...

nowadays deep excavations are needed for construction of foundation of high rise buildings, providing space for parking and etc. in some cases deep excavations may be constructed in the vicinity of the subway tunnels and causes unpredicted extra displacements and internal forces in tunnel lining of tunnels which were not designed for them and consequently affect serviceability of tunnel. theref...

the construction of underground tunnel plays a more and more important role in the development of big cities. one of the most important problems caused by the construction of the tunnel is that underground excavation will cause large settlement of the ground and buildings. previous studied showed the difference between numerical and experimental results. in this study the case study of niyayesh...