INTRODUCTION Primary adenocarcinoma of the seminal vesicle is an extremely rare condition. Some cases have been described in relation to congenital seminal vesicle cysts, which is often also associated with agenesia or ipsilateral renal disgenesia. The rareness of this type of lesions makes it difficult to plan a regulated surgical approach for them, although they are often treated by simple ex...

Agenesis of the inferior vena cava is a rare malformation. Its most common cause is dysgenesis during embryogenesis, but it may also be related to intrauterine or perinatal thrombosis. It is usually asymptomatic, associated or not with other congenital malformations and may be related to increased risk of chronic venous insufficiency and deep vein thrombosis, especially in young individuals. Di...

Introdução: A síndrome de Herlyn-Werner-Wunderlich (SHWW) é uma anomalia mülleriana rara, caracterizada por útero didelfo, septo hemivaginal e agenesia renal. Este relato, proveniente do serviço ginecologia infanto-puberal Hospital Universitário Clementino Fraga Filho (HUCFF), traz paciente com diagnóstico provável SHWW, os achados característicos as complicações típicas, que aguarda cirurgia. ...

The ductus venosus regulates the distribution of oxygen and placental nutrients by restricting the centralization of blood flow in fetal circulation. The ductus venosus is a small vein transmitting oxygen-rich blood from the umbilical vein to the fetal heart.. Increasing numbers of case reports are being published about ductus venosus agenesis with cardiac structural abnormalities, other malfor...

opsy was also performed in the left inferior conjunctival fornix of the mother’s eye to exclude ocular cicatricial pemphigoid. The biopsy specimen showed a nonspecific monocytic infiltration and epithelial squamous metaplasia. Direct immunofluorescence results were negative for IgG, IgM, IgA, and complement factors (C3 and C4). As expected, magnetic resonance imaging showed marked hypoplasia or...

Introduction Aglossia is a rare condition caused by failure of the tongue embryogenesis process (in the fourth to eighth weeks of gestation). The tongue is an organ used in different activities such as sucking, swallowing, chewing, and talking. It is also responsible for shaping palate dental arches (in its absence, they become atrophic). There are few similar cases reported in the literature. ...