OBJECTIVE Congenital diaphragmatic hernia is one of the severe congenital pulmonary anomaly (PA) associated with pulmonary hypoplasia, pulmonary sequestration and severe respiratory distress. The aim of this study was to present difference between measurements of the size of fetal pulmonary artery and pulmonary branches (PB) in normal growth fetuses and comparison with the same in fetuses with ...

Congenital thoracic malformations constitute a heterogeneous group of developmental disorders, involving lung parenchyma, arterial supply, and venous drainage.(1) Their etiology is embryologic, and their clinical presentation and severity vary according to the degree of pulmonary involvement and their location in the thoracic cavity.(2) They can be asymptomatic—their diagnosis being based on in...

We present the case of a 3-month-old infant with tetralogy of Fallot (ToF) with pulmonary artery hypoplasia, critical right ventricle outflow tract (RVOT) obstruction and the presence of major aortopulmonary collateral arteries (MAPCA) and CATCH 22 syndrome. Due to anatomical conditions (severe pulmonary artery hypoplasia), the patient was not qualified for palliative operative treatment Blaloc...

Hypoplasia of the right ventricle is uncommon as an isolated entity. It may result from tricuspid atresia, but is most commonly secondary to pulmonary atresia with intact ventricular septum. Pulmonary atresia with intact ventricular septum is rare, accounting for 1-3% of cases of congenital heart disease. It occurs in 0.1 to 0.4 in 10,000 live births. Pulmonary atresia with intact ventricular s...

The combination of pulmonary agenesis and anophtalmia or microphthalmia has been described previously. This condition is known as Matthew-Wood syndrome and PDAC syndrome (pulmonary hypoplasia/ agenesis, diaphragmatic hernia/eventration, anophthalmia/microphthalmia, and cardiac defect). We report a sporadic case of female infant with the combination of bilateral microphthalmia, unilateral right ...

The pulmonary function of ten adult patients with congenital pulmonary valvular stenosis was investigated. The patients clearly showed smaller lungs than healthy control subjects of equivalent age and height; lung elastic recoil pressure was normal at any given percentage of measured total lung capacity, indicating that postnatal parenchymal damage is not the cause of the small lungs. The lung ...

OBJECTIVE To determine pulmonary artery variations and other associated cardiac defects in patients with Tetralogy of Fallot (TOF). STUDY DESIGN Cross-sectional, descriptive study. PLACE AND DURATION OF STUDY The Children's Hospital and the Institute of Child Health, Lahore, from April 2006 to October 2007. METHODOLOGY All patients with TOF, who underwent cardiac catheterization during th...