A twenty-three-year-old male truck driver with a 12-pack year smoking history and no previous of hospitalization was admitted to the “Shefqet Ndroqi” University Hospital pulmonology department after cardiologist consultation where he diagnosed pulmonary hypertension. Two patient’s uncles from his mother’s side died during their pediatric age congenital heart defects. contrast-enhanced chest com...

Unilateral pulmonary agenesis is a medical condition characterized by the unilateral absence of pulmonary artery (UAPA). It is a rare congenital condition caused by malformation of pulmonary vascular system. Such patients often develop other congenital heart diseases, such as Tetralogy of Fallot, patent ductus arteriosus. In this report, we have described a 56-year-old male patient, who experie...

parents and sibling Fourthly, there was no family history suggestive of methemoglobinemia and methemoglobrn levels of both the parents and elder sibling were normal Fifthly, There is transient physiologic deficiency of cytochrome b5 reductive activity in neonates approximately 60% of the normal adult value, and even greater reduction in premature neonates is known making them more susceptible t...

Lung agensis is a rare developmental anomaly. It can range from total bronchial and parechymal agensis to mild pulmonary parenchymal hypoplasia of one or both lungs. A case of lobar agenesis of the left upper lung in a 15-year-old boy is presented. The patient had mild exertional dyspnea. Pulmonary angiography revealed the absence of the left upper pulmonary artery and vein. Bronchography showe...

Unilateral pulmonary artery agenesis is commonly seen associated with other congenital cardiovascular defects, when it is detected early in life, but isolated absence of the pulmonary artery is a rare entity, usually detected in adulthood. The latter patients are usually asymptomatic or might present with varied non-specific manifestations such as respiratory tract infections and hemoptysis. Th...

Isolated unilateral pulmonary artery agenesis is a rare congenital anomaly that may be complicated with hemoptysis, recurrent pulmonary infections or pulmonary hypertension. To our knowledge the occurrence of a coronary syndrome associated with a coronary-to-bronchial artery saccular aneurysmal collateralization has never been described before. A 44-year-old female presented a congenital right ...

BACKGROUND Unilateral pulmonary artery agenesis (UPAA) is a rare congenital anomaly due to a malformation of the sixth aortic arch of the affected side during embryogenesis. The diagnosis is usually set at adolescence, however it can remain asymptomatic and late diagnosis is possible. DESCRIPTION We present a case series of three female patients, aged 18, 49 and 68 years old, with history of ...