نتایج جستجو برای: prkar1a protein

تعداد نتایج: 1234776  

Journal: :Archives of Iranian medicine 2015
Yan Li Zhang Xiao Cong Wang Wei Yu Li Ping Pei Yan Ma Shu Jiang Yun Peng Sun

Carney complex is a syndrome characterized by skin pigmentation abnormalities, myxomas, endocrine tumors/overactivity, and schwannomas. It is caused by a mutation in the PRKAR1A gene that encodes the enzyme protein kinase A regulatory subunit type 1 alpha. A 23-year old male was diagnosed with Carney complex on the basis of spotty skin lentigines on his face and lips, multiple thyroid neoplasms...

Journal: :American journal of human genetics 2012
Hane Lee John M Graham David L Rimoin Ralph S Lachman Pavel Krejci Stuart W Tompson Stanley F Nelson Deborah Krakow Daniel H Cohn

Acrodysostosis is a dominantly-inherited, multisystem disorder characterized by skeletal, endocrine, and neurological abnormalities. To identify the molecular basis of acrodysostosis, we performed exome sequencing on five genetically independent cases. Three different missense mutations in PDE4D, which encodes cyclic AMP (cAMP)-specific phosphodiesterase 4D, were found to be heterozygous in thr...

1992
Kyung Mook Choi Jae Hong Seu Yong Hyun Kim Eun Jong Lee Sang Jin Kim Sei Hyun Baik Dong Seop Choi

A 12.5-year-old girl with diabetes mellitus type 1 presented with stunted growth and an increase in body weight. Also, her blood-sugar levels were difficult to manage. An adrenocorticotropin-(ACTH)-independent form of Cushing's syndrome was diagnosed. During the dexamethasone-suppression test, a paradoxical increase in urinary-free cortisol excretion was observed, which is a clear indication of...

Journal: :The Journal of Thoracic and Cardiovascular Surgery 2016

پایان نامه :وزارت علوم، تحقیقات و فناوری - دانشگاه تربیت مدرس - دانشکده کشاورزی 1391

aflp یک ابزار قدرتمند برای تشخیص رونوشت هایی با فراوانی کم است و می تواند بعنوان یک روش کارآمد برای جداسازی ژنهایی که بطور متمایز بیان می شوند، بکار رود. بنابراین القا متمایز ژنها در گندم ( رقم چمران و مرودشت) در پاسخ به قارچ m.graminicola بوسیله آنالیز cdna-aflp مورد مطالعه قرار گرفت . در ابتدا گیاهان بوسیله بیمارگر مایه زنی شدند. نمونه برداری در 6 نقطه زمانی(0، 12، 24، 48، 72 و 96 ساعت) بعد ا...

Journal: :The Journal of clinical endocrinology and metabolism 2004
Daniel F Gunther Isabelle Bourdeau Ludmila Matyakhina David Cassarino David E Kleiner Kurt Griffin Nickolas Courkoutsakis Mones Abu-Asab Maria Tsokos Meg Keil J Aidan Carney Constantine A Stratakis

Cushing syndrome is uncommon in childhood and rare in infancy. We report the case of a 3-yr-old child who presented with symptoms of Cushing syndrome beginning shortly after birth. Her hypercortisolemia was cyclical, causing relapsing and remitting symptoms, which eventually led to suspicions of possible Munchausen syndrome by proxy. Investigation at the National Institutes of Health excluded e...

Journal: :Endocrinology, Diabetes & Metabolism Case Reports 2019

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