Aim : to present a clinical case of pancreatic PEComa with liver metastases an emphasis on morphological features, radiology diagnostic methods and features treatment tactics, allowing practitioners get idea about this rare mesenchymal tumors composed “perivascular epithelioid cells”, review literature data PEComa, including 32 author's cases. General statements . A 22-year-old woman who was su...

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/ by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited. Perivascular epithelioid cell tumor (PEComa) is an extremely rare mesenchymal tumor, which ...

Perivascular epithelioid cell tumors are soft tissue tumors that can occur in various locations in the body whose incidence is rising. Hepatic PEComas are quite rare and diagnosis involves positivity of Melan-A and HMB45 on immunohistochemistry. Usual treatment is surgery for benign tumors and chemotherapy including mTOR inhibitors for malignant tumors. Here we discuss the radiological and path...

BACKGROUND Perivascular epithelioid cell tumors (PEComas) are a rare group of neoplasms composed of epithelioid cells that express both melanocytic and myoid markers. When considering PEComas of the female genital tract, the uterus is the most common location. Involvement of the ovary in the context of a primary uterine PEComa, in the absence of systemic disease associated with tuberous scleros...