The granulomatosis with polyangiitis (GPA), formerly known as Wegener’s granulomatosis, is a pauci-immune vasculitis involving small- and medium-sized blood vessels. Classically, the patients inflicted with this disease present with a triad of necrotizing granulomatous inflammation of the respiratory tract, cutaneous necrotizing vasculitis, and glomerulonephritis (GN). The antinuclear (ANA) and...

how to cite this article: salehi omran mr, nooreddini h, baghdadi f. acute necrotizing encephalopathy of childhood; a case report. iran j child neurol. 2013 spring;7(2):51-54.   abstract acute necrotizing encephalopathy of childhood (anec) is an atypical disease followed by respiratory or gastrointestinal infection, high fever, which is accompanied with rapid alteration of consciousness and sei...